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Cystic Fibrosis

Known as: MUCOVISCIDOSIS, Cystic fibrosis NOS, disease fibrocystic pancreas 
A congenital, autosomal, metabolic disorder affecting the exocrine glands. The secretions of exocrine glands are abnormal, resulting in excessively… 
National Institutes of Health

Related topics

Related topics

47 relations
AcetylcysteineAcetylcysteine 200 MG/ML Inhalant SolutionAdenocarcinoma of the ileumAmiloride Hydrochloride

Broader (4)

Congenital DisordersLung diseasesMetabolic Diseasesairway disease

Narrower (3)

Cystic Fibrosis with Helicobacter Pylori Gastritis, Megaloblastic Anemia, and Subnormal MentalityFibrocystic Disease of PancreasLubani Al Saleh Teebi syndrome

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2005
Highly Cited
2005
Increased arginase activity in cystic fibrosis airways.
RATIONALE Airway nitric oxide concentrations are reduced in cystic fibrosis (CF). Arginases compete for L-arginine, the substrate… 
Highly Cited
2004
Highly Cited
2004
Inflammation of the cystic fibrosis mouse small intestine.
The CFTR null mouse [cystic fibrosis (CF) mouse] has a severe intestinal phenotype that serves as a model for CF-related growth… 
Highly Cited
2003
Highly Cited
2003
Chloride transport across vesicle and cell membranes by steroid-based receptors.
We therefore supposed that electroneutralcholapods might transport inorganic anions bya “shuttle”mechanism… 
Highly Cited
2000
Highly Cited
2000
Bone density, body composition, and inflammatory status in cystic fibrosis.
Low body weight and loss of bone mass are major problems in adults with cystic fibrosis (CF) and chronic pulmonary infection… 
Review
1999
Review
1999
Large-scale production of pharmaceutical-grade plasmid DNA for gene therapy: problems and bottlenecks.
Highly Cited
1998
Highly Cited
1998
Nitrite levels in breath condensate of patients with cystic fibrosis is elevated in contrast to exhaled nitric oxide
BACKGROUND Nitric oxide (NO) is released by activated macrophages, neutrophils, and stimulated bronchial epithelial cells… 
Highly Cited
1996
Highly Cited
1996
Airway nitric oxide in asthmatic children and patients with cystic fibrosis.
We evaluated the effects of asthma and cystic fibrosis on nitric oxide (NO) concentrations in the respiratory tract. NO levels in… 
Highly Cited
1988
Highly Cited
1988
Altered intestinal chloride transport in cystic fibrosis
Sodium ion and chloride transport was studied in vitro in small intestinal and colonic tissue from patients with cystic fibrosis… 
Highly Cited
1988
Highly Cited
1988
Allergy in asthma. I. The dose relationship of allergy to severity of childhood asthma.
Review
1986
Review
1986
Pseudomonas cepacia: biology, mechanisms of virulence, epidemiology.
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