Cystic Fibrosis

Known as: Mucoviscidosis, Cystic fibrosis NOS, disease fibrocystic pancreas 
A congenital, autosomal, metabolic disorder affecting the exocrine glands. The secretions of exocrine glands are abnormal, resulting in excessively… (More)

Topic mentions per year

Topic mentions per year

1938-2017
01000200019382016

Papers overview

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Review
2014
Review
2014
Aspergillus fumigatus isolation in cultures from respiratory specimens of patients with cystic fibrosis (CF) is quite common… (More)
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Highly Cited
2011
Highly Cited
2011
BACKGROUND Increasing the activity of defective cystic fibrosis transmembrane conductance regulator (CFTR) protein is a potential… (More)
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Highly Cited
2008
Highly Cited
2008
Newborn screening (NBS) for cystic fibrosis (CF) is increasingly being implemented and is soon likely to be in use throughout the… (More)
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Highly Cited
2006
Highly Cited
2006
In many human infections, hosts and pathogens coexist for years or decades. Important examples include HIV, herpes viruses… (More)
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Highly Cited
2000
Highly Cited
2000
The bacterium Pseudomonas aeruginosa permanently colonizes cystic fibrosis lungs despite aggressive antibiotic treatment. This… (More)
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Highly Cited
2000
Highly Cited
2000
The lungs of cystic fibrosis (CF) patients are chronically infected for years by one or a few lineages of Pseudomonas aeruginosa… (More)
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Highly Cited
1990
Highly Cited
1990
The gene associated with cystic fibrosis (CF) encodes a membrane-associated, N-linked glycoprotein called CFTR. Mutations were… (More)
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Highly Cited
1989
Highly Cited
1989
Overlapping complementary DNA clones were isolated from epithelial cell libraries with a genomic DNA segment containing a portion… (More)
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Highly Cited
1989
Highly Cited
1989
Approximately 70 percent of the mutations in cystic fibrosis patients correspond to a specific deletion of three base pairs… (More)
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Highly Cited
1989
Highly Cited
1989
An understanding of the basic defect in the inherited disorder cystic fibrosis requires cloning of the cystic fibrosis gene and… (More)
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