West Syndrome

Known as: Lightning spasms, Attacks, Lightning, Attack, Lightning 
An epileptic syndrome characterized by the triad of infantile spasms, hypsarrhythmia, and arrest of psychomotor development at seizure onset. The… (More)
National Institutes of Health

Papers overview

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Highly Cited
2013
Highly Cited
2013
  • 2013
Epileptic encephalopathies are a devastating group of severe childhood epilepsy disorders for which the cause is often unknown… (More)
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Highly Cited
2013
Highly Cited
2013
OBJECTIVE We aimed to investigate the possible association between SCN2A mutations and early-onset epileptic encephalopathies… (More)
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Highly Cited
2007
Highly Cited
2007
Early infantile epileptic encephalopathy with suppression-burst pattern (EIEE) is one of the most severe and earliest forms of… (More)
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Review
2006
Review
2006
There is a remarkable array of new chemical entities in the current antiepileptic drug (AED) development pipeline. In some cases… (More)
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Highly Cited
2005
Highly Cited
2005
BACKGROUND Rett syndrome is a severe neurodevelopmental disorder, almost exclusively affecting females and characterised by a… (More)
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Review
2004
Review
2004
PURPOSE To reach a broad consensus on case definitions, outcomes, and outcome measures that will ease future study design and… (More)
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Review
2004
Review
2004
Epilepsy is very common in tuberous sclerosis complex and occurs in 80 to 90% of affected individuals during their lifetime… (More)
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Highly Cited
2001
Highly Cited
2001
UNLABELLED In a representative series of 53 females with Rett syndrome (RS), aged 5-55 y, a history of epilepsy was present in 50… (More)
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Highly Cited
1996
Highly Cited
1996
Neurological complications and other causes of morbidity were studied in 122 of 131 individuals (64 males, 67 females) with… (More)
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Highly Cited
1989
Highly Cited
1989
Preface Since the Proposal for Classification of Epilepsies and Epileptic Syndromes was presented to the General Assembly of the… (More)
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