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Porphyrias, Hepatic
Known as:
Hepatic Porphyrias
, Hepatic Porphyria
, Porphyrias, Hepatic [Disease/Finding]
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A group of metabolic diseases due to deficiency of one of a number of LIVER enzymes in the biosynthetic pathway of HEME. They are characterized by…
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National Institutes of Health
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Related topics
Related topics
14 relations
Narrower (6)
Acute intermittent porphyria
Cafe-au-lait macules with pulmonary stenosis
Coproporphyria
Porphobilinogen synthase deficiency
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Broader (2)
Disorders of Porphyrin Metabolism
Liver diseases
In Blood
Microbiological
chemically induced
nursing therapy
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Papers overview
Semantic Scholar uses AI to extract papers important to this topic.
1987
1987
[Drug risk of hepatic porphyria. Development of an animal experiment model].
J. Deybach
,
V. Da Silva
,
L. Phung
,
J. Lévy
,
Y. Nordmann
Presse medicale
1987
Corpus ID: 8118550
Hepatic porphyrias (acute intermittent porphyria, coproporphyria, porphyria variegata and porphyria cutanea) are inherited…
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1986
1986
[Acute attacks of hepatic porphyria. Treatment with hematin. 5 cases].
J. F. Devars du Mayne
,
J. Deybach
,
+4 authors
Y. Nordmann
Presse medicale
1986
Corpus ID: 44258269
The effectiveness of 2 hematins administered by intravenous infusion was compared in acute intermittent porphyria. Judging from…
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1985
1985
Sn-protoporphyrin suppresses chemically induced experimental hepatic porphyria. Potential clinical implications.
R. Galbraith
,
G. Drummond
,
A. Kappas
Journal of Clinical Investigation
1985
Corpus ID: 33519966
The ability of Sn(tin)-protoporphyrin to inhibit the induction of hepatic delta-aminolevulinate (ALA) synthase by allylisopropyl…
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1982
1982
Environmental and drug factors in hepatic porphyria.
D. Bickers
Acta Dermato-Venereologica Supplementum
1982
Corpus ID: 40425422
Numerous drugs and environmental chemicals are capable of influencing the clinical expression of human hepatic porphyria…
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1982
1982
Environmental and drug factors in hepatic porphyria.
Bickers Dr
1982
Corpus ID: 78328083
Numerous drugs and environmental chemicals are capable of influencing the clinical expression of human hepatic porphyria…
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1979
1979
Haem biosynthesis in cutaneous hepatic porphyria: comparison with alcoholism and liver disease.
M. Brodie
,
G. Thompson
,
+4 authors
J. Hunter
Acta hepato-gastroenterologica
1979
Corpus ID: 22285059
The enzymes of haem biosynthesis have been measured in the peripheral blood of 13 patients with cutaneous hepatic porphyria. The…
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1978
1978
Uroporphyrinogen Decarboxylase (Uro-D) Defect in Erythrocytes in Chronic Hepatic Porphyrias
R. Tiepermann
,
M. Doss
1978
Corpus ID: 74619139
The accumulation of porphyrins in liver tissue and the profile of porphyrins excreted in the urine, both characteristic for…
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1976
1976
Hepatic haem metabolism in porphyria cutanea tarda (PCT): enzymatic studies and their relation to liver ultrastructure.
G. Blekkenhorst
,
N. Pimstone
,
B. Webber
,
L. Eales
Annals of clinical research
1976
Corpus ID: 23317551
Hepatic levels of cytochrome P-450 are elevated more than 4-fold in porphyria cutanea tarda (PCT) but not in other hepatic…
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1973
1973
Hereditary hepatic porphyrias.
U. Meyer
,
R. Schmid
Federation proceedings
1973
Corpus ID: 27959694
1962
1962
Experimental hepatic porphyria caused by feeding 3,5-diethoxycarbonyl-1,4-dihydro-2,4,6-trimethylpyridine. Comparison with sedormid porphyria.
F. de Matteis
,
B. Prior
Biochemical Journal
1962
Corpus ID: 6949624
Since Schmid & Schwartz (1952) described an experimental hepatic porphyria induced in rabbits by Sedormid (2-isopropylpent-4…
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