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Disorders of Porphyrin Metabolism

Known as: Disorders, Porphyrin, porphyrinopathies, porphyrinopathy 
A diverse group of metabolic diseases characterized by errors in the biosynthetic pathway of HEME in the LIVER, the BONE MARROW, or both. They are… 
National Institutes of Health

Related topics

Related topics

50 relations
84 HR Estradiol 0.00208 MG/HR Transdermal System [Vivelle]84 HR Estradiol 0.00313 MG/HR Transdermal System [Vivelle]84 HR Estradiol 0.00417 MG/HR Transdermal System [Estraderm]Amobarbital Sodium

Narrower (4)

Chester-type porphyriaErythropoietic ProtoporphyriaPorphyria, ErythropoieticYusho Disease

Broader (2)

Hematological Diseasehepatobiliary disease

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2003
Highly Cited
2003
A mono-TTF-annulated porphyrin as a fluorescence switch.
Annulation of one TTF unit directly to the porphyrin chromophore produces an almost nonfluorescent species which can be… 
Highly Cited
2001
Highly Cited
2001
Supramolecular assemblies between macrocyclic porphyrin hexamers and star-shaped porphyrin arrays.
The syntheses of eight new star-shaped D(3)-symmetric arrays in which three 15-(pyrid-4-yl)porphyrin subunits are attached to the… 
Highly Cited
1996
Highly Cited
1996
Porphyrin metalation catalyzed by a small RNA molecule
We report here the isolation and characterization of a 35-nucleotide (nt) RNA that catalyzes the related Cu(II) insertion into… 
Highly Cited
1980
Highly Cited
1980
Dependence of the porphyrogenic effect of 2,3,7,8-tetrachlorodibenzo(p)dioxin upon inheritance of aryl hydrocarbon hydroxylase responsiveness.
Highly Cited
1977
Highly Cited
1977
Effects of pentachlorophenol on hepatic drug-metabolizing enzymes and porphyria related to contamination with chlorinated dibenzo-p-dioxins and dibenzofurans.
Highly Cited
1973
Highly Cited
1973
STUDIES IN PORPHYRIA
Patients with the genetic liver disease, acute intermittent porphyria (AIP), have a defect in the reductive transformation of… 
Highly Cited
1972
Highly Cited
1972
Decreased levels of cytochrome P-450 and catalase in hepatic porphyria caused by substituted acetamides and barbiturates. Importance of the allyl group in the molecule of the active drugs.
Review
1970
Review
1970
Harderoporphyrin: a new porphyrin from the Harderian glands of the rat.
Highly Cited
1959
Highly Cited
1959
Tryptophan metabolism in porphyria, schizophrenia, and a variety of neurologic and psychiatric diseases
PATIENTS WITH ACUTE hepatic porphyria frequently have an increased urinary excretion of zinc, while patients with mixed and… 
Highly Cited
1950
Highly Cited
1950
Studies in congenital porphyria. 2. Incorporation of 15N in the stercobilin in the normal and in the porphyric.
In man, hippuric acid is formed mainly in the liver. This organ contains appreciable amounts of -free glycine and other… 
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