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Neuronal Ceroid-Lipofuscinoses

Known as: Diseases, Ceroid Storage, Ceroid Storage Diseases, Neuronal Ceroid-Lipofuscinoses [Disease/Finding] 
A group of severe neurodegenerative diseases characterized by intracellular accumulation of autofluorescent wax-like lipid materials (CEROID… 
National Institutes of Health

Related topics

Related topics

22 relations

Narrower (13)

Adult Neuronal Ceroid LipofuscinosisCEROID LIPOFUSCINOSIS, NEURONAL, 1CEROID LIPOFUSCINOSIS, NEURONAL, 2CEROID LIPOFUSCINOSIS, NEURONAL, 5

Broader (3)

Cerebral lipidosesLipoidosisMental Retardation
In BloodMicrobiologicalchemically inducednursing therapy

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2013
Highly Cited
2013
Central nervous system stem cell transplantation for children with neuronal ceroid lipofuscinosis.
OBJECT Infantile and late-infantile neuronal ceroid lipofuscinoses (NCLs) are invariably fatal lysosomal storage diseases… 
Review
2004
Review
2004
Selectivity and Types of Cell Death in the Neuronal Ceroid Lipofuscinoses (NCLs)
Cloning of the individual genes that are mutated in neuronal cerold lipofuscinoses (NCLs), or Batten disease, has opened up new… 
Review
1999
Review
1999
Mutant mice with scrambled brains: understanding the signaling pathways that control cell positioning in the CNS.
The characterization of mouse neurological mutants has proven to be an extremely valuable approach to the analysis of central… 
Highly Cited
1993
Highly Cited
1993
Dormancy of inhibitory interneurons in a model of temporal lobe epilepsy.
In humans temporal lobe epilepsy (TLE) is characterized by recurrent seizures, neuronal hyperexcitability, and selective loss of… 
Highly Cited
1987
Highly Cited
1987
Cerebellum and Neuronal Plasticity
Structure and Function of the Cerebellum.- Parasagittal Zonation of the Cerebellum in Macaques: An analysis based on… 
Highly Cited
1986
Highly Cited
1986
A reversible type of neuronal injury following ischemia in the gerbil hippocampus.
The Mongolian gerbil is known to develop delayed neuronal death in the hippocampus following brief forebrain ischemia (Brain Res… 
Highly Cited
1986
Highly Cited
1986
Synapsin I: A synaptic vesicle-associated neuronal phosphoprotein
Highly Cited
1982
Highly Cited
1982
In vitro Evidence for two distinct hippocampal growth factors: basis of neuronal plasticity?
The rat hippocampal formation was tested for the presence of factors that would accelerate neurite extension from chick… 
Highly Cited
1978
Highly Cited
1978
Identification of pyramidal cells as the critical elements in hippocampal neuronal plasticity during learning.
The activity of single neurons recorded from rabbit hippocampus during classical conditioning of the nictitating membrane reflex… 
Highly Cited
1971
Highly Cited
1971
Neuronal hyperactivity in experimental trigeminal deafferentation.
✓ Postoperative facial paresthesias frequently occur in patients following retrogasserian rhizotomy. To investigate the etiology… 
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