High molecular weight kininogen deficiency

Known as: Fitzgerald factor deficiency, Williams factor deficiency, HMWK Deficiency 
A rare autosomal recessive inherited disorder characterized by prolonged partial thromboplastin time and absence of bleeding diathesis.
National Institutes of Health

Papers overview

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Highly Cited
2012
Highly Cited
2012
Financial market imperfections severely restrict international trade ‡ows because exporters require external capital. This paper… (More)
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Highly Cited
2009
Highly Cited
2009
Changes in glycosylation, most notably fucosylation, have been associated with the development of hepatocellular carcinoma (HCC… (More)
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Highly Cited
2007
Highly Cited
2007
Data on international relative prices from industrialized countries show large and systematic deviations from relative purchasing… (More)
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Highly Cited
2006
Highly Cited
2006
The phosphoinositide 3-kinase (PI3K)/Akt pathway is commonly activated in cancer; therefore, we investigated its role in hypoxia… (More)
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Highly Cited
2003
Highly Cited
2003
We posit that limited transparency of firms’ operations to outside investors increases demands on governance systems to alleviate… (More)
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2001
2001
A 66 year old male, referred for cardiac surgery, was found to have high molecular weight kininogen deficiency (activity <1… (More)
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1986
1986
High mol wt kininogen (HMWK), the major cofactor-substrate of the contact phase of coagulation, is contained within and secreted… (More)
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1980
1980
Plasma from individuals with high molecular weight (HMW) kininogen deficiency has been reported to be deficient in prekallikrein… (More)
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1976
1976
Plasma from an asymptomatic person with defects in blood coagulation, release of kinin, and evolution of fibrinolytic activity… (More)
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Highly Cited
1975
Highly Cited
1975
An asymptomatic woman (Ms. Williams) was found to have a severe abnormality in the surface-activated intrinsic coagulation… (More)
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