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ethylmalonic acid
Known as:
1,1-Propanedicarboxylic acid
, alpha-carboxybutyric acid
, propanedioic acid, ethyl-
National Institutes of Health
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2 relations
Broader (1)
Malonates
Narrower (1)
ethylmalonate
Papers overview
Semantic Scholar uses AI to extract papers important to this topic.
2016
2016
Ethylmalonic encephalopathy associated with respiratory failure
H. Köse
,
M. Şahan
,
H. Aydın
2016
Corpus ID: 56440333
2016
2016
Ionic conductance of ethylmalonic acid
R. Holze
2016
Corpus ID: 104355278
2012
2012
Arabidopsis ETHE 1 Encodes a Sulfur Dioxygenase That Is Essential for Embryo and Endosperm Development 1 [ C ] [ OA ]
Meghan M. Holdorf
,
H. Owen
,
+4 authors
C. Makaroff
2012
Corpus ID: 36277608
Mutations in human (Homo sapiens) ETHYLMALONIC ENCEPHALOPATHY PROTEIN1 (ETHE1) result in the complex metabolic disease…
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2012
2012
ETHYLMALONIC ACIDURIA AND REPORT OF ONE CASE FROM IRAN
P. Karimzadeh
2012
Corpus ID: 56518882
This condition is due to deficiency in electron transport flavoprotein or electron transport fluvoprotein dehydrogenase.The…
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2010
2010
Exercise testing in patients with short- chain acyl-CoA dehydrogenase deficiency: biochemical responses and effects of riboflavin therapy
B. T. V. Maldegem
,
M. Durán
,
H. Waterham
,
T. Koning
,
F. Wijburg
2010
Corpus ID: 74659153
Short-chain acyl-CoA dehydrogenase deficiency (SCADD) is a mitochondrial fatty acid oxidation disorder, most frequently…
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2009
2009
MITOCHONDRIAL CYTOPATHIES IN CHILDREN AND ADULTS
M. Tarnopolsky
2009
Corpus ID: 74787628
Mitochondrial cytopathies represent a heterogenous group of disorders with abnormal mitochondrial structure or function as the…
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2001
2001
Metabolism in Rats in Viuo of RS-2-Methylbutyrate and n-Butyrate Labeled with Stable Isotopes at Various Positions
Bruce
,
H. Baretz
,
Charles
,
P. Lollo
2001
Corpus ID: 40599019
[l-‘3C]Butyric acid and four different racemic 2-methylbutyric acids labeled with 13C or ‘H at various positions were synthesized…
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1978
1978
Investigation of the mechanism of the methylmalonyl-CoA mutase reaction with the substrate analogue: ethylmalonyl-CoA.
J. Rétey
,
E. Smith
,
B. Zagalak
European Journal of Biochemistry
1978
Corpus ID: 35869386
1. Ethylmalonyl-CoA was found to be a substrate for methylmalonyl-CoA mutase from Propionibacterium shermanii, the product being…
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1978
1978
538 ETHYLMALONIC-ADIPIC ACIDURIA: A NEW DEFECT OF BUTYRATE OXIDATION ASSOCIATED WITH HYPOGLYCEMIA
S. Mantaqos
,
V. Genel'
,
K. Tanaka
,
L. Rosenberg
Pediatric Research
1978
Corpus ID: 20527153
A 5 year old girl with recurrent hypoglycemia, acidosis and normal development was found to excrete in her urine massive…
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Highly Cited
1976
Highly Cited
1976
Demonstration of a new mammalian isoleucine catabolic pathway yielding an Rseries of metabolites.
O. Mamer
,
S. Tjoa
,
C. Scriver
,
G. Klassen
Biochemical Journal
1976
Corpus ID: 38382232
1. Normal human urine contains small amounts (less than 4 mg/g of creatinine) of 2-ethylhydracrylic acid, formed, we believe, by…
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