Skip to search formSkip to main contentSkip to account menu

Prion Diseases

Known as: Prion-Associated Disorders, Transmissible Dementia, Prion Disease 
A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases… 
National Institutes of Health

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2010
Highly Cited
2010
Recombinant Infectious Prions Prion diseases are a group of fatal neurodegenerative disorders that include Creutzfeldt-Jakob… 
Highly Cited
2005
Highly Cited
2005
Neurodegenerative diseases such as Alzheimer's, Parkinson's and the transmissible spongiform encephalopathies (TSEs) are… 
Review
2001
Review
2001
  • J. Collinge
  • Annual review of neuroscience
  • 2001
  • Corpus ID: 18915904
Prion diseases are transmissible neurodegenerative conditions that include Creutzfeldt-Jakob disease (CJD) in humans and bovine… 
Highly Cited
2000
Highly Cited
2000
The NMR structures of the recombinant human prion protein, hPrP(23-230), and two C-terminal fragments, hPrP(90-230) and hPrP(121… 
Highly Cited
1998
Highly Cited
1998
At the endoplasmic reticulum membrane, the prion protein (PrP) can be synthesized in several topological forms. The role of these… 
Review
1997
Review
1997
Bovine spongiform encephalopathy (BSE) and human Creutzfeldt-Jakob disease (CJD) are among the most notable central nervous… 
Highly Cited
1997
Highly Cited
1997
Epidemiological and clinicopathological studies, allied with pathological prion protein (PrPSc) analysis, strongly support the… 
Highly Cited
1996
Highly Cited
1996
The fundamental event in prion diseases seems to be a conformational change in cellular prion protein (PrPC) whereby it is… 
Review
1991
Review
1991
Prions cause transmissible and genetic neurodegenerative diseases, including scrapie and bovine spongiform encephalopathy of… 
Highly Cited
1991
Highly Cited
1991
THE human prion diseases, Creutzfeldt–Jakob disease (CJD) and Gerstmann–Sträussler syndrome (GSS), are neurodegenerative diseases…