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Prion Diseases
Known as:
Prion-Associated Disorders
, Transmissible Dementia
, Prion Disease
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A group of genetic, infectious, or sporadic degenerative human and animal nervous system disorders associated with abnormal PRIONS. These diseases…
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National Institutes of Health
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Related topics
Related topics
25 relations
Central Nervous System
Communicable Diseases
Corticostriatal-Spinal Degeneration
Dementia
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Narrower (4)
Creutzfeldt-Jakob disease
Gerstmann-Straussler-Scheinker Disease
Kuru
SPONGIFORM ENCEPHALOPATHY WITH NEUROPSYCHIATRIC FEATURES
Broader (1)
Organic brain syndrome
Papers overview
Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2010
Highly Cited
2010
Generating a Prion with Bacterially Expressed Recombinant Prion Protein
Fei Wang
,
Xinhe Wang
,
C. Yuan
,
Jiyan Ma
Science
2010
Corpus ID: 52859827
Recombinant Infectious Prions Prion diseases are a group of fatal neurodegenerative disorders that include Creutzfeldt-Jakob…
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Highly Cited
2005
Highly Cited
2005
The most infectious prion protein particles
J. Silveira
,
G. J. Raymond
,
+4 authors
B. Caughey
Nature
2005
Corpus ID: 10356603
Neurodegenerative diseases such as Alzheimer's, Parkinson's and the transmissible spongiform encephalopathies (TSEs) are…
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Review
2001
Review
2001
Prion diseases of humans and animals: their causes and molecular basis.
J. Collinge
Annual review of neuroscience
2001
Corpus ID: 18915904
Prion diseases are transmissible neurodegenerative conditions that include Creutzfeldt-Jakob disease (CJD) in humans and bovine…
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Highly Cited
2000
Highly Cited
2000
NMR solution structure of the human prion protein.
R. Zahn
,
A. Liu
,
+7 authors
K. Wüthrich
Proceedings of the National Academy of Sciences…
2000
Corpus ID: 17206423
The NMR structures of the recombinant human prion protein, hPrP(23-230), and two C-terminal fragments, hPrP(90-230) and hPrP(121…
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Highly Cited
1998
Highly Cited
1998
A transmembrane form of the prion protein in neurodegenerative disease.
R. Hegde
,
J. Mastrianni
,
+6 authors
V. Lingappa
Science
1998
Corpus ID: 20176119
At the endoplasmic reticulum membrane, the prion protein (PrP) can be synthesized in several topological forms. The role of these…
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Review
1997
Review
1997
Prion diseases and the BSE crisis.
S. Prusiner
Science
1997
Corpus ID: 14326354
Bovine spongiform encephalopathy (BSE) and human Creutzfeldt-Jakob disease (CJD) are among the most notable central nervous…
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Highly Cited
1997
Highly Cited
1997
The same prion strain causes vCJD and BSE
A. Hill
,
M. Desbruslais
,
+5 authors
P. Lantos
Nature
1997
Corpus ID: 1670201
Epidemiological and clinicopathological studies, allied with pathological prion protein (PrPSc) analysis, strongly support the…
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Highly Cited
1996
Highly Cited
1996
Evidence for the Conformation of the Pathologic Isoform of the Prion Protein Enciphering and Propagating Prion Diversity
G. Telling
,
Piero Parchi
,
+7 authors
S. Prusiner
Science
1996
Corpus ID: 27670762
The fundamental event in prion diseases seems to be a conformational change in cellular prion protein (PrPC) whereby it is…
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Review
1991
Review
1991
Molecular biology of prion diseases
S. Prusiner
Science
1991
Corpus ID: 22417182
Prions cause transmissible and genetic neurodegenerative diseases, including scrapie and bovine spongiform encephalopathy of…
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Highly Cited
1991
Highly Cited
1991
Homozygous prion protein genotype predisposes to sporadic Creutzfeldt–Jakob disease
M. Palmer
,
A. J. Dryden
,
J. T. Hughes
,
J. Collinge
Nature
1991
Corpus ID: 4261434
THE human prion diseases, Creutzfeldt–Jakob disease (CJD) and Gerstmann–Sträussler syndrome (GSS), are neurodegenerative diseases…
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