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Gerstmann-Straussler-Scheinker Disease

Known as: Gerstmann Straussler Scheinker Syndrome, Gerstmann-Straussler-Scheinker Syndrome, Gerstmann-Straussler Inherited Spongiform Encephalopathy 
An autosomal dominant familial prion disease with a wide spectrum of clinical presentations including ATAXIA, spastic paraparesis, extrapyramidal… 
National Institutes of Health

Papers overview

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2007
2007
Amyloid fibrils in Gerstmann–Sträussler–Scheinker (GSS) disease are composed of a fragment of the prion protein (PrP), the N and… 
Highly Cited
1993
Highly Cited
1993
Gerstmann-sträussler-Scheinker disease in the Indiana kindred is pathologically characterized by deposits of PrP-amyloid… 
1993
1993
We report the first family among the Jewish population in Israel with Gerstmann-Straussler-Scheinker disease. A proline-for… 
Review
1991
Review
1991
Kuru and the transmissible virus dementias Creutzfeldt-Jakob disease (CJD) and Gerstmann-Straussler-Scheinker syndrome (GSS… 
1990
1990
A comparison was made of the effects of experimental intracerebral inoculation into marmosets of brain homogenates from a case of…