Creutzfeldt-Jakob disease

Known as: Classic Creutzfeldt-Jakob Disease, CJD (Creutzfeldt-Jakob Disease), Creutzfeldt-Jakob Syndrome [Disease/Finding] 
A rare transmissible encephalopathy most prevalent between the ages of 50 and 70 years. Affected individuals may present with sleep disturbances… (More)
National Institutes of Health

Papers overview

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Highly Cited
2004
Highly Cited
2004
BACKGROUND Variant Creutzfeldt-Jakob disease (vCJD) is a novel human prion disease caused by infection with the agent of bovine… (More)
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Highly Cited
2003
Highly Cited
2003
According to the protein-only hypothesis of prion propagation, an abnormal isoform (designated PrP(Sc)) of the cellular prion… (More)
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Review
2000
Review
2000
The causes and geographic distribution of 267 cases of iatrogenic Creutzfeldt-Jakob disease (CJD) are here updated at the… (More)
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Highly Cited
2000
Highly Cited
2000
As of December 31, 1998, 35 deaths had been attributed to new variant Creutzfeldt-Jakob disease (nvCJD) in the United Kingdom, of… (More)
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Highly Cited
1999
Highly Cited
1999
Phenotypic heterogeneity in sporadic Creutzfeldt-Jakob disease (sCJD) is well documented, but there is not yet a systematic… (More)
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Review
1999
Review
1999
It is clear that the prion strain causing bovine spongiform encephalopathy (BSE) in cattle has infected human beings, manifesting… (More)
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Highly Cited
1996
Highly Cited
1996
BACKGROUND Epidemiological surveillance of Creutzfeldt-Jakob disease (CJD) was reinstituted in the UK in 1990 to identify any… (More)
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Highly Cited
1996
Highly Cited
1996
We sequenced the prion protein gene and studied the biochemical characteristics and the intracerebral distribution of protease… (More)
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Highly Cited
1995
Highly Cited
1995
Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease (CJD) and other human transmissible spongiform… (More)
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Highly Cited
1991
Highly Cited
1991
The spongiform encephalopathy Creutzfeldt-Jakob disease (CJD) has been transmitted to man via administration of growth hormone… (More)
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