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GLUCOSYLCERAMIDASE

Known as: Lysosomal Glucocerebrosidase, beta Glucocerebrosidase, D-Glucosyl-N-Acylsphingosine Glucohydrolase 
A glycosidase that hydrolyzes a glucosylceramide to yield free ceramide plus glucose. Deficiency of this enzyme leads to abnormally high… 
National Institutes of Health

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Narrower (3)

AbcertinGBA1 protein, zebrafishimiglucerase
Acid beta glucosidase:CCnc:Pt:Bld.dot:QnAcid beta glucosidase:CCnt:Pt:Fibroblasts:QnAcid beta glucosidase:CCnt:Pt:WBC:QnAcid beta glucosidase:CCnt:Pt:XXX:Qn

Papers overview

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Review
2007
Review
2007
Therapy of adult Gaucher disease.
Gaucher disease, the most common lysosomal storage disease, is caused by an autosomal-recessively inherited deficiency of… 
2005
2005
The treatment of Gaucher disease in countries with limited health care resources
Indian Journal of Human Genetics September-December 2005 Volume 11 Issue 3 Gaucher disease is probably the most common of the… 
1986
1986
A kinetic study of the effects of galactocerebroside 3-sulphate on human spleen glucocerebrosidase. Evidence for two activator-binding sites.
Extraction of control human spleen glucocerebrosidase with sodium cholate and butan-l-ol reversibly inactivates the enzyme in… 
1986
1986
Studies on the turnover of glucocerebrosidase in cultured rat peritoneal macrophages and normal human fibroblasts.
The kinetics of glucocerebrosidase synthesis and degradation in rat peritoneal macrophages and in human fibroblasts have been… 
1986
1986
Preliminary evidence for a processing error in the biosynthesis of Gaucher activator in mucolipidosis disease types II and III.
Activator protein (AP), which stimulated fibroblast sphingomyelinase activity, was isolated from the spleen of a patient with… 
1985
1985
High-resolution proton nuclear magnetic resonance studies of the glucocerebrosidase activator protein from Gaucher spleen.
A heat-stable protein factor (HSF) obtained from the spleen of a patient with Gaucher's disease that activates glucocerebrosidase… 
1983
1983
Electron microscopic study on the structures formed by mixtures containing synthetic glyceroglycolipids.
Structures of aqueous dispersions prepared from monoglycosyldiglycerides and from mixtures of monoglycosyldiglyceride and… 
Highly Cited
1982
Highly Cited
1982
Glucocerebroside transfer between phosphatidylcholine bilayers.
We have studied the kinetics of transfer of glucocerebroside between phospholipid bilayers by using pyrene and 3H-labeled… 
1982
1982
Purification of glucosylceramidase by affinity chromatography.
Glucosylceramide: beta-glucosidase (glucocerebrosidase, EC 3.2.1.45) has been purified 12 900-fold from human placenta using a… 
1979
1979
L-glucosylceramide: synthesis, properties, and resistance to catabolism by glucocerebrosidase in vitro.
Procedures for the synthesis and radioactive labeling of L-glucosylceramide are described. This compound is a stereoisomeric…