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Carglumic acid

Known as: (S)-2-ureidopentanedioic acid, N-Carbamyl-L-glutamate, Ureidoglutaric acid 
An orally active, synthetic structural analogue of N-acetylglutamate (NAG) and carbamoyl phosphate synthetase 1 (CPS 1) activator, with ammonia… 
National Institutes of Health

Related topics

Related topics

5 relations

Narrower (1)

Carbaglu
Carbamoyl Phosphate Synthetase 1 Activators [MoA]Carglumic acid 200 MG Tablet for Oral Suspension [Carbaglu]N-carbamylglutamate

Broader (1)

Glutamates

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Review
2017
Review
2017
[Treatment of encephalopathy by means of valproic acid with carglumic acid: two case reports and a review of the literature].
INTRODUCTION Valproic acid (VPA) is a drug mainly used to treat epilepsy. Hyperammonaemic encephalopathy due to VPA is a rare but… 
2016
2016
Hyperinsulinism Hyperammonemia Syndrome, a Rare Clinical Constellation
We present the unique case of adult hyperinsulinism hyperammonemia syndrome (HI/HA). This condition is rarely seen in children… 
2015
2015
From pair quadruple- to single-stranded helices to lines in a mixed ligand system via adjusting the N-substituent of L-Glu.
Utilizing the mixed-ligand strategy, a novel fourfold-interpenetrated 3D homochiral metal-organic framework (1) with rare pair… 
2015
2015
Challenges in optimizing sample preparation and LC-MS/MS conditions for the analysis of carglumic acid, an N-acetyl glutamate derivative in human plasma.
This paper describes a systematic approach to overcoming challenges in developing a robust and selective liquid chromatography… 
2013
2013
Late optic neuropathy in propionic acidemia following surgical intervention.
T raber et al (1) recently reported a case of “Subacute bilateral visual loss in methylmalonic acidemia” in a 23-year-old woman… 
2010
2010
Carglumic acid approved to treat genetic hyperammonemia.
FDA on March 18 approved the marketing of carglumic acid, or Carbaglu, for the treatment of a rare genetic enzyme deficiency that… 
1989
1989
Synthesis of p-aminohippuric acid analog and its labeling by technetium-99m.
1963
1963
Biosynthesis of riboflavin (Vit. B2) by eremothecium ashbyii
Summary1.Of the various carbon sources tested, glucose proved to be among the most suitable for both growth and flavinogenesis.2… 
1963
1963
Biosynthesis of riboflavin (Vit. B2) by eremothecium ashbyii
Summary1.The cis-forms of higher, unsaturated fatty acids, oleic and erucic markedly stimulated riboflavin synthesis while the… 
1955
1955
The basis of the carbamate reaction.
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