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N-carbamylglutamate

Known as: N-carbamoylglutamate, carbamylglutamate 
National Institutes of Health

Related topics

Related topics

2 relations
Carglumic acid

Broader (1)

Glutamates

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Review
2016
Review
2016
Dietary arginine and N-carbamylglutamate supplementation enhances the antioxidant statuses of the liver and plasma against oxidative stress in rats.
N-Carbamylglutamate (NCG), an effective precursor of arginine (ARG), can enhance ARG synthesis, increase intestinal growth, and… 
Review
2016
Review
2016
N-acetylglutamate synthase deficiency: Novel mutation associated with neonatal presentation and literature review of molecular and phenotypic spectra
2016
2016
Urinary Metabolomic Approach Provides New Insights into Distinct Metabolic Profiles of Glutamine and N-Carbamylglutamate Supplementation in Rats
Glutamine and N-carbamylglutamate can enhance growth performance and health in animals, but the underlying mechanisms are not yet… 
2016
2016
Hyperammonemia due to Adult-Onset N-Acetylglutamate Synthase Deficiency.
A 59-year-old woman, with a medical history of intellectual disability after perinatal asphyxia, was admitted because of coma due… 
2011
2011
N‐carbamylglutamate enhancement of ureagenesis leads to discovery of a novel deleterious mutation in a newly defined enhancer of the NAGS gene and to effective therapy
N‐acetylglutamate synthase (NAGS) catalyzes the conversion of glutamate and acetyl‐CoA to NAG, the essential allosteric activator… 
Highly Cited
2010
Highly Cited
2010
Favourable long-term outcome after immediate treatment of neonatal hyperammonemia due to N-acetylglutamate synthase deficiency
IntroductionN-Acetylglutamate synthase (NAGS) deficiency is a rare urea cycle disorder, which may present in the neonatal period… 
2009
2009
The first use of N-carbamylglutamate in a patient with decompensated maple syrup urine disease
Maple syrup urine disease (MSUD) is a defect in the catabolism of the branched-chain amino acids; leucine, isoleucine, and valine… 
Review
2004
Review
2004
Mammalian N-acetylglutamate synthase.
1996
1996
Therapeutic use of carbamylglutamate in the case of carbamoyl-phosphate synthetase deficiency
Ammonia is channelled into the urea cycle by means of carbamoyl-phosphate synthetase (CPS I). This initial step of urea synthesis… 
1992
1992
Treatment of hyperammonemia with carbamylglutamate in rats
A protein‐free diet causes a paradoxical increase of blood ammonia levels that seems to be due to decreased liver content of… 
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