Known as: PAPA syndrome is an acronym for Pyogenic sterile Arthritis, Pyoderma gangrenosum, Acne, PAPA, Pyogenic Sterile Arthritis, Pyoderma Gangrenosum, and Acne
An autoinflammatory disease caused by mutations in the PSTPIP1 gene. It is characterized by episodes of destructive arthritis, ulcerative skin…