Pyogenic Arthritis, Pyoderma Gangrenosum and Acne

Known as: PAPA syndrome is an acronym for Pyogenic sterile Arthritis, Pyoderma gangrenosum, Acne, PAPA, Pyogenic Sterile Arthritis, Pyoderma Gangrenosum, and Acne 
An autoinflammatory disease caused by mutations in the PSTPIP1 gene. It is characterized by episodes of destructive arthritis, ulcerative skin… (More)
National Institutes of Health

Papers overview

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2013
2013
Pyogenic Arthritis, Pyoderma Gangrenosum, and Acne Syndrome (PAPA syndrome) is an autoinflammatory disease caused by aberrant… (More)
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Highly Cited
2012
Highly Cited
2012
OBJECTIVE To describe the genotypes, phenotypes, immunophenotypes, and treatments of PAPA syndrome (pyogenic sterile arthritis… (More)
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Highly Cited
2012
Highly Cited
2012
BACKGROUND PAPA syndrome is a recently identified hereditary autoinflammatory syndrome clinically characterized by pyogenic… (More)
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Highly Cited
2009
Highly Cited
2009
The triad of sterile pyogenic arthritis, pyoderma gangrenosum and acne is known by the acronym of PAPA syndrome. It is a rare… (More)
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Highly Cited
2007
Highly Cited
2007
Inflammatory bowel disease (IBD) mainly affects the gastrointestinal system but is associated with various chronic diseases of… (More)
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2002
2002
Pyogenic aseptic arthritis, pyoderma gangrenosum, and cystic acne (PAPA) syndrome is an unusual triad that was recently mapped to… (More)
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Highly Cited
2001
Highly Cited
2001
OBJECTIVE:The aim of this study was to determine the prevalence of the major extraintestinal manifestations of inflammatory bowel… (More)
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2000
2000
Pyoderma gangrenosum, cystic acne, and aseptic arthritis are clinically distinct disorders within the broad class of inflammatory… (More)
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Highly Cited
1997
Highly Cited
1997
OBJECTIVE To describe a multigenerational family with transmission of an autosomal dominant disorder characterized by pyogenic… (More)
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Review
1996
Review
1996
Pyoderma gangrenosum (PG) has four distinctive clinical and histologic variants. Some have morphologic and histologic overlapping… (More)
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