Skip to search formSkip to main contentSkip to account menu

triheptanoin

Known as: glyceroltriheptanoate, glyceryl triheptanoate 
National Institutes of Health

Related topics

Related topics

1 relation

Broader (1)

Triglycerides

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Review
2017
Review
2017
Metabolic Dysfunctions in Amyotrophic Lateral Sclerosis Pathogenesis and Potential Metabolic Treatments
Amyotrophic lateral sclerosis (ALS) is a fatal neurodegenerative disease primarily characterized by loss of motor neurons in… 
Review
2016
Review
2016
Current Pharmacological Approaches to Reduce Chorea in Huntington’s Disease
There are currently no effective pharmacological agents available to stop or prevent the progression of Huntington’s disease (HD… 
Highly Cited
2015
Highly Cited
2015
Triheptanoin dramatically reduces paroxysmal motor disorder in patients with GLUT1 deficiency
Objective On the basis of our previous work with triheptanoin, which provides key substrates to the Krebs cycle in the brain, we… 
Highly Cited
2014
Highly Cited
2014
Triheptanoin for glucose transporter type I deficiency (G1D): modulation of human ictogenesis, cerebral metabolic rate, and cognitive indices by a food supplement.
IMPORTANCE Disorders of brain metabolism are multiform in their mechanisms and manifestations, many of which remain… 
2014
2014
Anaplerotic Triheptanoin Diet Enhances Mitochondrial Substrate Use to Remodel the Metabolome and Improve Lifespan, Motor Function, and Sociability in MeCP2-Null Mice
Rett syndrome (RTT) is an autism spectrum disorder (ASD) caused by mutations in the X-linked MECP2 gene that encodes methyl-CpG… 
Review
2012
Review
2012
GLUT1 deficiency syndrome in clinical practice
  • J. Klepper
  • Epilepsy Research
  • 2012
  • Corpus ID: 43104780
Review
2010
Review
2010
Disorders of muscle lipid metabolism: Diagnostic and therapeutic challenges
Highly Cited
2005
Highly Cited
2005
Ingested medium-chain fatty acids are directly utilized for the acyl modification of ghrelin.
Ghrelin, an acylated brain and gut peptide, is primarily produced by endocrine cells of the gastric mucosa for secretion into the… 
Highly Cited
2005
Highly Cited
2005
Pyruvate carboxylase deficiency: clinical and biochemical response to anaplerotic diet therapy.
Highly Cited
2002
Highly Cited
2002
Treatment of cardiomyopathy and rhabdomyolysis in long-chain fat oxidation disorders using an anaplerotic odd-chain triglyceride.
The current dietary treatment of long-chain fatty acid oxidation defects (high carbohydrate with medium-even-chain triglycerides… 
By clicking accept or continuing to use the site, you agree to the terms outlined in our Privacy Policy (opens in a new tab), Terms of Service (opens in a new tab), and Dataset License (opens in a new tab)