methylmalonate

 
National Institutes of Health

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2013
2013
BACKGROUND Methylmalonate semialdehyde dehydrogenase (MMSDH) deficiency is a rare autosomal recessive disorder with varied… (More)
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2012
2012
PURPOSE Methylmalonic acidemias are inherited metabolic disorders characterized by methylmalonate (MMA) accumulation and… (More)
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2007
2007
Methylene blue (MB) is a thiazine dye with cationic and lipophilic properties that acts as an electron transfer mediator in the… (More)
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2007
2007
The effect of methylmalonate (MMA) on mitochondrial succinate oxidation has received great attention since it could present an… (More)
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2006
2006
Methylmalonic acidemias are metabolic disorders caused by a severe deficiency of methylmalonyl CoA mutase activity, which are… (More)
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2006
2006
Homotetrameric MSDH (methylmalonate semialdehyde dehydrogenase) from Bacillus subtilis catalyses the NAD-dependent oxidation of… (More)
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Highly Cited
2000
Highly Cited
2000
Buffered methylmalonate (MMA) was injected s.c. into rats twice a day at 8 h intervals from 5 to 25 days of age (chronic… (More)
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1998
1998
Several inhibitors of mitochondrial complex II cause neuronal death in vivo and in vitro. The goal of the present work was to… (More)
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1992
1992
A 5417-base pair (bp) region of Pseudomonas aeruginosa PAO chromosomal DNA containing the mmsAB operon and an upstream regulatory… (More)
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1991
1991
1. Methylmalonate (MMA) levels (2.0-2.5 mM) comparable to those of human methylmalonic acidemia were achieved in blood of young… (More)
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