fibrillin-2

Known as: Fibrillin 2, Fibrillin-2 [Chemical/Ingredient] 
A fibrillin (FBN2) that functions to regulate the assembly of ELASTIC FIBERS. Mutations in the FBN2 gene are associated with congenital contractural… (More)
National Institutes of Health

Topic mentions per year

Topic mentions per year

1994-2018
05101519942018

Papers overview

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Highly Cited
2009
Highly Cited
2009
Fibrillins constitute the major backbone of multifunctional microfibrils in elastic and nonelastic extracellular matrices. Proper… (More)
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2007
2007
LTBP-2 is a matrix protein of unknown function since, unlike other LTBPs, it does not form covalent complexes with latent TGF… (More)
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Highly Cited
2006
Highly Cited
2006
Fibrillin-rich microfibrils are extracellular assemblies that impart structural properties to the connective tissue. To elucidate… (More)
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2003
2003
Fibrillin-1 and -2 are large modular extracellular matrix glycoproteins found in many vertebrate organ systems and are known to… (More)
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2002
2002
Fibrillin-1 and fibrillin-2 constitute the backbone of extracellular filaments, called microfibrils. Fibrillin assembly involves… (More)
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Highly Cited
1996
Highly Cited
1996
The fibrillins are large glycoprotein components of 10-nm microfibrils found in the extracellular matrix of most tissues… (More)
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Highly Cited
1995
Highly Cited
1995
Extracellular microfibrils, alone or in association with elastin, confer critical biomechanical properties on a variety of… (More)
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Highly Cited
1995
Highly Cited
1995
Congenital contractural arachnodactyly (CCA) is an autosomal dominant disorder that is phenotypically similar to Marfan syndrome… (More)
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1995
1995
The recent characterization of multiple fibrillin genes raises the question of whether each of the fibrillin proteins is a… (More)
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Highly Cited
1994
Highly Cited
1994
During the previous cloning of the fibrillin gene (FBN1), we isolated a partial cDNA coding for a fibrillin-like peptide and… (More)
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