Profibrillin 1

Known as: Profibrillin-1

National Institutes of Health

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.

1995

1995

Truncated profibrillin of a Marfan patient is of apparent similar size as fibrillin: intracellular retention leads to over-N-glycosylation.

We studied profibrillin-1 (proFib) synthesis and microfibril formation in cultured fibroblasts from an individual with severe…