FAQ

Dementia, familial British

Known as: FBD, Presenile dementia with spastic ataxia, Cerebral amyloid angiopathy, British type 
 
National Institutes of Health

Topic mentions per year

Topic mentions per year

1984-2018
05101519842018

Related topics

Related topics

1 relation

Broader (1)

Familial Cerebral Amyloid Angiopathy

Related mentions per year

Related mentions per year

1983-2018
19801990200020102020
Dementia, familial British
Familial Cerebral Amyloid Angiopathy

Papers overview

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Highly Cited
2015
Highly Cited
2015
World Health Organization Global Estimates and Regional Comparisons of the Burden of Foodborne Disease in 2010.
Illness and death from diseases caused by contaminated food are a constant threat to public health and a significant impediment… (More)
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2010
2010
Memory deficits due to familial British dementia BRI2 mutation are caused by loss of BRI2 function rather than amyloidosis.
Familial dementias, which include Alzheimer disease (AD), familial British dementia (FBD), and familial Danish dementia (FDD… (More)
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Highly Cited
2005
Highly Cited
2005
The familial dementia BRI2 gene binds the Alzheimer gene amyloid-beta precursor protein and inhibits amyloid-beta production.
Alzheimer disease (AD), the most common senile dementia, is characterized by amyloid plaques, vascular amyloid, neurofibrillary… (More)
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Highly Cited
2003
Highly Cited
2003
Cognitive-behavioral therapy versus education and desipramine versus placebo for moderate to severe functional bowel disorders.
BACKGROUND & AIMS Studies of antidepressants and psychological treatments in functional bowel disorders (FBD) are… (More)
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2003
2003
Expression of BRI, the normal precursor of the amyloid protein of familial British dementia, in human brain
Familial British dementia (FBD) is characterized neuropathologically by deposition of a unique amyloid-forming protein, ABri. It… (More)
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Highly Cited
2002
Highly Cited
2002
BRICHOS: a conserved domain in proteins associated with dementia, respiratory distress and cancer.
A novel domain (the BRICHOS domain) of approximately 100 amino acids has been identified in several previously unrelated proteins… (More)
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2002
2002
Proteolytic processing of familial British dementia-associated BRI variants: evidence for enhanced intracellular accumulation of amyloidogenic peptides.
Different mutations in the BRI(2) gene cause rare neurodegenerative conditions, termed familial British dementia (FBD) and… (More)
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2001
2001
Systemic amyloid deposits in familial British dementia.
Familial British dementia (FBD) is an early onset inherited disorder that, like familial Alzheimer's disease (FAD), is… (More)
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2001
2001
Regional distribution of amyloid-Bri deposition and its association with neurofibrillary degeneration in familial British dementia.
Familial British dementia (FBD), pathologically characterized by cerebral amyloid angiopathy (CAA), amyloid plaques, and… (More)
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Highly Cited
1999
Highly Cited
1999
A stop-codon mutation in the BRI gene associated with familial British dementia.
Familial British dementia (FBD), previously designated familial cerebral amyloid angiopathy-British type, is an autosomal… (More)
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