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3-methylbutyrylcarnitine

Known as: isovalerylcarnitine 
 
National Institutes of Health

Papers overview

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2016
2016
BACKGROUND The analysis of dried blood spots has been used routinely for newborn screening since the early 1970s, and the number… Expand
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2009
2009
Activation of the peroxisome proliferator-activated receptor alpha (PPARalpha) is associated with increased fatty acid catabolism… Expand
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2007
2007
Tandem mass spectrometry (MS/MS) has become a prominent method for screening newborns for diseases such as organic acidemia and… Expand
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2006
2006
AIM To determine the plasma carnitine ester profile in adult patients with ulcerative culitis (UC) and compared with healthy… Expand
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2000
2000
A searchable library of MS/MS spectra obtained using a quadrupole ion trap mass spectrometer and electrospray or atmospheric… Expand
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1996
1996
Acylcarnitines in amniotic fluid samples were analyzed for the prenatal diagnosis of propionic acidemia, methylmalonic aciduria… Expand
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1995
1995
The Milan hypertensive strain (MHS) of rats, in addition to having hypertension, is also characterized by a genetic deficiency in… Expand
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1986
1986
The profound metabolic disturbances which occur in isovaleric acidaemia are due to the intramitochondrial accumulation of… Expand
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Highly Cited
1984
Highly Cited
1984
ABSTRACT: Concentrations of l-carnitine and acylcarnitines have been determined in urine from patients with disorders of organic… Expand
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1984
1984
Isovaleric acidemia, resulting from isovaleryl-coenzyme A dehydrogenase deficiency, is associated with marked reduction of free… Expand
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