3-methylbutyrylcarnitine

Known as: isovalerylcarnitine 
 
National Institutes of Health

Topic mentions per year

Topic mentions per year

1979-2017
02419792017

Papers overview

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2010
2010
BACKGROUND Flow-injection MS/MS methods for elevated acylcarnitines are routinely performed in most newborn screening and… (More)
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2009
2009
Activation of the peroxisome proliferator-activated receptor alpha (PPARalpha) is associated with increased fatty acid catabolism… (More)
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2007
2007
Crohn's disease (CD) is a chronic inflammatory bowel disorder caused by environmental and genetic factors. The purpose of this… (More)
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2007
2007
Tandem mass spectrometry (MS/MS) has become a prominent method for screening newborns for diseases such as organic acidemia and… (More)
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1998
1998
Tandem mass spectrometric analysis of acylcarnitines and amino acids has been applied in newborn screening programmes for the… (More)
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1996
1996
OBJECTIVE To assess the effectiveness of glycine and carnitine therapy on isovaleryl conjugate excretion in isovaleric acidemia… (More)
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1990
1990
Isovalerylcarnitine, a product of the catabolism of L-leucine, is a potent activator of rat calpains isolated from erythrocytes… (More)
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1986
1986
The profound metabolic disturbances which occur in isovaleric acidaemia are due to the intramitochondrial accumulation of… (More)
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Highly Cited
1984
Highly Cited
1984
ABSTRACT: Concentrations of l-carnitine and acylcarnitines have been determined in urine from patients with disorders of organic… (More)
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1984
1984
Isovaleric acidemia, resulting from isovaleryl-coenzyme A dehydrogenase deficiency, is associated with marked reduction of free… (More)
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