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tetrahydrobiopterin metabolic process

Known as: 5,6,7,8-tetrahydrobiopterin metabolic process, tetrahydrobiopterin metabolism 
The chemical reactions and pathways involving tetrahydrobiopterin, the reduced form of biopterin (2-amino-4-hydroxy-6-(1,2-dihydroxypropyl)-pteridine… 
National Institutes of Health

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
2017
2017
Altered tetrahydrobiopterin metabolism in patients with phenylalanine hydroxylase deficiency
AbstractThe tetrahydrobiopterin (BH4) cofactor is essential for the activity of various enzymes, including phenylalanine (Phe… 
2007
2007
Nitric oxide accelerates the degradation of tetrahydrobiopterin but not total neopterin in cerebrospinal fluid; potential implications for the assessment of tetrahydrobiopterin metabolism
Assessment of total neopterin and tetrahydrobioterin (BH4) concentrations in cerebrospinal fluid (CSF) can be used to identify… 
2000
2000
Abnormalities in urinary pterin levels in Rett syndrome.
The pterins, neopterin and biopterin, occur naturally in body fluids including urine. Increased neopterin levels are associated… 
1988
1988
Problems in the diagnosis of tetrahydrobiopterin deficiency
Sir: Following the paper by Niederwieser et al. [3] on peripheral tetrahydrobiopterin deficiency with hyperphenylalaninaemia due… 
Review
1988
Review
1988
Hyperphenylalaninemia syndromes: current status of diagnosis and management.
The phenylalanine hydroxylating system and its related disorders have been intensely investigated during the past decade. This… 
1988
1988
The effects of some neurotoxins on tetrahydrobiopterin metabolism
Previous studies in man have shown that following dosing with L--3,4-dihydroxyphenylalanine (L-DOPA) and cotrimoxazole, plasma… 
1986
1986
Unsolved problems in diagnosis and therapy of hyperphenylalaninemia caused by defects in tetrahydrobiopterin metabolism.
1986
1986
The effect of lead on tetrahydrobiopterin metabolism. A possible mechanism for neurotoxicity.
1986
1986
Partial dihydropteridine reductase deficiency and mental retardation
A complete deficiency of dihydropteridine reductase (DHPR, EC 1.6.99.7) leads to severe mental retardation… 
1985
1985
Tetrahydrobiopterin metabolism in the Rett disease
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