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gamma-butyrobetaine,2-oxoglutarate dioxygenase activity

Known as: 4-trimethylammoniobutanoate,2-oxoglutarate:oxygen oxidoreductase (3-hydroxylating), g-butyrobetaine dioxygenase activity, gamma-butyrobetaine hydroxylase activity 
Catalysis of the reaction: 2-oxoglutarate + 4-(trimethylammonio)butanoate + O(2) = carnitine + CO(2) + succinate. [EC:1.14.11.1, RHEA:24031]
National Institutes of Health

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
2002
2002
Research Article Thyroid hormone controls carnitine status through modifications of g-butyrobetaine hydroxylase activity and gene expression
The carnitine system plays a key role in b-oxi- dation of long-chain fatty acids by permitting their trans- port into the… 
2001
2001
Carnitine Biosynthesis from y-Butyrobetaine and from Exogenous Protein-bound 6N-Trimethyl-~-lysine by the Perfused Guinea Pig Liver
The production of carnitine from peptide-bound 6N-trimethyl-L-lysine (Lys(Me3)) or 4-N-trimethylaminobutyrate (y-butyrobetaine… 
1991
1991
[The effect of mildronate on carnitine-dependent and carnitine-independent ketogenesis in rats].
Mildronate of 3-(2,2,2-trimethylhydrozinium)propionate, a novel anti-ischemic drug, inhibits the biosynthesis of carnitine from Y… 
Highly Cited
1980
Highly Cited
1980
Clofibrate enhancement of mitochondrial carnitine transport system of rat liver and augmentation of liver carnitine and gamma-butyrobetaine hydroxylase activity by thyroxine.
1978
1978
A simplified method for the measurement of y-butyrobetaine hydroxylase activity
Summary A method for the assay of y-butyrobetaine hydroxylase activity is described. The procedure is based on the measurement of… 
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