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beta-hydroxyisovaleric acid

Known as: beta-hydroxy-beta-methylbutyrate, 3-hydroxyisovaleric acid, HMB-d6 
National Institutes of Health

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3-Hydroxyisovalerate

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Papers overview

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2005
2005
Studies toward a conjugate vaccine for anthrax. Synthesis and characterization of anthrose [4,6-dideoxy-4-(3-hydroxy-3-methylbutanamido)-2-O-methyl-D-glucopyranose] and its methyl glycosides.
1999
1999
Differential effects of biotin deficiency and replenishment on rat liver pyruvate and propionyl-CoA carboxylases and on their mRNAs.
Although the role of vitamins as prosthetic groups of enzymes is well known, their participation in the regulation of their… 
1992
1992
Familial hypotonia of childhood caused by isolated 3-methylcrotonyl-coenzyme A carboxylase deficiency.
1990
1990
3-Hydroxy-3-methylglutaryl-CoA lyase deficiency as detected by radiochemical assay in cell extracts by thin-layer chromatography, and identification of three new cases.
In this rapid radiochemical assay for 3-hydroxy-3-methylglutaryl-coenzyme A lyase (I) activity in cell extracts, DL-3[glutaryl-3… 
1989
1989
Quantification of urinary 3-hydroxyisovaleric acid using deuterated 3-hydroxyisovaleric acid as internal standard.
Deficiency of biotin at the tissue level can be assessed indirectly by measuring the urinary excretion of 3-hydroxyisovaleric… 
1982
1982
Gas-chromatographic/mass spectrometric detection of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in double first cousins.
Gas chromatography/mass spectrometry was used for the detection of 3-hydroxy-3-methylglutaryl-CoA lyase (EC 4.1.3.4) deficiency… 
1981
1981
Biotin-responsive in vivo carboxylase deficiency in two siblings with secretory diarrhea receiving total parenteral nutrition.
1976
1976
Application of glass capillary-column gas chromatography-mass spectrometry to the studies of human diseases.
1976
1976
Massive excretion of 2-oxoglutaric acid and 3-hydroxyisovaleric acid in a patient with a deficiency of 3-methylcrotonyl-CoA carboxylase.
1974
1974
Increased urinary excretion of 3-hydroxyisovaleric acid in patients with ketoacidosis.
  • S. Landaas
  • Clinica chimica acta; international journal of…
  • 1974
  • Corpus ID: 10195423
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