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atrophin-1
Known as:
DRPLA protein
, dentatorubral-pallidoluysian atrophy protein
National Institutes of Health
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Related topics
Related topics
3 relations
ATN1 gene
Narrower (1)
Drpla protein, rat
Broader (1)
Nerve Tissue Proteins
Papers overview
Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2006
Highly Cited
2006
Nuclear receptor TLX prevents retinal dystrophy and recruits the corepressor atrophin1.
Chun-Li Zhang
,
Y. Zou
,
R. Yu
,
F. Gage
,
R. Evans
Genes & development
2006
Corpus ID: 21833428
During mammalian embryogenesis, precise coordination of progenitor cell proliferation and differentiation is essential for proper…
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Highly Cited
2006
Highly Cited
2006
Histone deacetylase-associating Atrophin proteins are nuclear receptor corepressors.
L. Wang
,
Harini Rajan
,
J. L. Pitman
,
M. McKeown
,
Chih-Cheng Tsai
Genes & development
2006
Corpus ID: 37921015
Drosophila Tailless (Tll) is an orphan nuclear receptor involved in embryonic segmentation and neurogenesis. Although Tll exerts…
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Highly Cited
2002
Highly Cited
2002
Drosophila Atrophin Homolog Functions as a Transcriptional Corepressor in Multiple Developmental Processes
S. Zhang
,
Lei Xu
,
J. Lee
,
T. Xu
Cell
2002
Corpus ID: 14605566
Dentatorubral-pallidoluysian atrophy is a progressive neurodegenerative disease caused by the expansion of a polyglutamine…
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Highly Cited
2002
Highly Cited
2002
Polyglutamine and transcription: gene expression changes shared by DRPLA and Huntington's disease mouse models reveal context-independent effects.
R. Luthi-Carter
,
A. Strand
,
+8 authors
J. Olson
Human molecular genetics
2002
Corpus ID: 12517662
Recent evidence indicates that transcriptional abnormalities may play an important role in the pathophysiology of polyglutamine…
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Highly Cited
2001
Highly Cited
2001
Widespread occurrence of intranuclear atrophin‐1 accumulation in the central nervous system neurons of patients with dentatorubral‐pallidoluysian atrophy
M. Yamada
,
J. D. Wood
,
+4 authors
H. Takahashi
Annals of neurology
2001
Corpus ID: 37415413
Dentatorubral‐pallidoluysian atrophy (DRPLA) is an autosomal dominant neurodegenerative disorder caused by a CAG repeat expansion…
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Highly Cited
2000
Highly Cited
2000
Atrophin-1, the Dentato-Rubral and Pallido-Luysian Atrophy Gene Product, Interacts with Eto/Mtg8 in the Nuclear Matrix and Represses Transcription
J. Wood
,
F. Nucifora
,
+7 authors
C. Ross
The Journal of cell biology
2000
Corpus ID: 9481474
Dentato-rubral and pallido-luysian atrophy (DRPLA) is one of the family of neurodegenerative diseases caused by expansion of a…
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Highly Cited
1999
Highly Cited
1999
Nuclear Accumulation of Truncated Atrophin-1 Fragments in a Transgenic Mouse Model of DRPLA
G. Schilling
,
J. Wood
,
+12 authors
C. Ross
Neuron
1999
Corpus ID: 14269445
Dentatorubral and pallidoluysian atrophy (DRPLA) is a member of a family of progressive neurodegenerative diseases caused by…
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Highly Cited
1999
Highly Cited
1999
Cleavage of Atrophin-1 at Caspase Site Aspartic Acid 109 Modulates Cytotoxicity*
L. Ellerby
,
R. Andrusiak
,
+9 authors
D. Bredesen
The Journal of Biological Chemistry
1999
Corpus ID: 8603554
Dentatorubropallidoluysian atrophy (DRPLA) is one of eight autosomal dominant neurodegenerative disorders characterized by an…
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Highly Cited
1998
Highly Cited
1998
Caspase Cleavage of Gene Products Associated with Triplet Expansion Disorders Generates Truncated Fragments Containing the Polyglutamine Tract*
C. Wellington
,
L. Ellerby
,
+18 authors
M. Hayden
The Journal of Biological Chemistry
1998
Corpus ID: 1825610
The neurodegenerative diseases Huntington disease, dentatorubropallidoluysian atrophy, spinocerebellar atrophy type 3, and spinal…
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Highly Cited
1998
Highly Cited
1998
Atrophin-1, the DRPLA Gene Product, Interacts with Two Families of WW Domain-Containing Proteins
J. Wood
,
J. Yuan
,
R. Margolis
,
V. Colomer
,
C. Ross
Molecular and Cellular Neuroscience
1998
Corpus ID: 20003277
Atrophin-1 contains a polyglutamine repeat, expansion of which is responsible for dentatorubral and pallidoluysian atrophy (DRPLA…
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