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atrophin-1

Known as: DRPLA protein, dentatorubral-pallidoluysian atrophy protein 
 
National Institutes of Health

Papers overview

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Highly Cited
2006
Highly Cited
2006
During mammalian embryogenesis, precise coordination of progenitor cell proliferation and differentiation is essential for proper… Expand
Highly Cited
2006
Highly Cited
2006
Drosophila Tailless (Tll) is an orphan nuclear receptor involved in embryonic segmentation and neurogenesis. Although Tll exerts… Expand
Highly Cited
2002
Highly Cited
2002
Dentatorubral-pallidoluysian atrophy is a progressive neurodegenerative disease caused by the expansion of a polyglutamine… Expand
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Highly Cited
2002
Highly Cited
2002
Recent evidence indicates that transcriptional abnormalities may play an important role in the pathophysiology of polyglutamine… Expand
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Highly Cited
2001
Highly Cited
2001
Dentatorubral‐pallidoluysian atrophy (DRPLA) is an autosomal dominant neurodegenerative disorder caused by a CAG repeat expansion… Expand
Highly Cited
2000
Highly Cited
2000
Dentato-rubral and pallido-luysian atrophy (DRPLA) is one of the family of neurodegenerative diseases caused by expansion of a… Expand
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Highly Cited
1999
Highly Cited
1999
Dentatorubral and pallidoluysian atrophy (DRPLA) is a member of a family of progressive neurodegenerative diseases caused by… Expand
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Highly Cited
1999
Highly Cited
1999
Dentatorubropallidoluysian atrophy (DRPLA) is one of eight autosomal dominant neurodegenerative disorders characterized by an… Expand
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Highly Cited
1998
Highly Cited
1998
The neurodegenerative diseases Huntington disease, dentatorubropallidoluysian atrophy, spinocerebellar atrophy type 3, and spinal… Expand
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Highly Cited
1998
Highly Cited
1998
Atrophin-1 contains a polyglutamine repeat, expansion of which is responsible for dentatorubral and pallidoluysian atrophy (DRPLA… Expand