FAQ

TEMPI Syndrome

A rare syndrome characterized by telangiectasias, elevated erythropoietin level and erythrocytosis, monoclonal gammopathy, perinephric fluid… (More)
National Institutes of Health

Topic mentions per year

Topic mentions per year

2011-2018
01220112018

Papers overview

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Review
2018
Review
2018
Complete Responses in the TEMPI Syndrome after Treatment with Daratumumab.
n engl j med 378;23 nejm.org June 7, 2018 2240 Germline inactivating SMARCA4 variants are driver mutations in malignant rhabdoid… (More)
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Review
2015
Review
2015
Bone marrow findings of the newly described TEMPI syndrome: when erythrocytosis and plasma cell dyscrasia coexist
TEMPI syndrome (telangiectasias, elevated erythropoietin level and erythrocytosis, monoclonal gammopathy, perinephric fluid… (More)
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2015
2015
Difficulties in hematopoietic progenitor cell collection from a patient with TEMPI syndrome and severe iatrogenic iron deficiency.
BACKGROUND Collection of hematopoietic progenitor cells by apheresis (HPC-A) requires separation of cells by density. Previous… (More)
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2014
2014
Subcutaneous bortezomib for treatment of TEMPI syndrome.
 
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2014
2014
Case report: a 37-year-old male with telangiectasias, polycythemia vera, perinephric fluid collections, and intrapulmonary shunting
BACKGROUND The TEMPI syndrome was recently described in 2011, and is characterized by the constellation of five hallmarks… (More)
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2012
2012
Bortezomib to treat the TEMPI syndrome.
n engl j med 366;19 nejm.org may 10, 2012 1843 ability. On the first point, thiazide diuretics or beta-blockers in addition to… (More)
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2012
2012
A new case of TEMPI syndrome
We present an interesting case of a woman with new onset hypertension and abdominal fullness who was found to have huge bilateral… (More)
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2012
2012
Complete and partial responses of the TEMPI syndrome to bortezomib.
n engl j med 367;8 nejm.org august 23, 2012 778 is one of the very few to have been published. This lack of data on the subject… (More)
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2011
2011
The TEMPI syndrome--a novel multisystem disease.
n engl j med 365;5 nejm.org august 4, 2011 475 patients who underwent a baseline bone marrow evaluation at the time of diagnosis… (More)
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2011
2011
The role of hypoxia-inducible factor-1 alpha in TEMPI syndrome
Sir, Two recent reports in The New England Journal of Medicine on a newly described syndrome, namely TEMPI syndrome… (More)
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