Hemophagocytic Syndrome

Known as: Hemophagocytic syndromes, haemophagocytic syndrome, haemophagocytic syndromes 
A classification of rare, non-neoplastic, proliferative disorders of the hematologic system. Primary or familial hemophagocytic lymphohistiocytosis… (More)
National Institutes of Health

Papers overview

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Highly Cited
2012
Highly Cited
2012
Familial hemophagocytic lymphohistiocytosis (FHL) is a life-threatening disorder of immune regulation caused by defects in… (More)
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Highly Cited
2006
Highly Cited
2006
Griscelli syndrome (GS) was diagnosed in a 2-year-old patient with oculocutaneous albinism and immunodeficiency, but sequencing… (More)
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Highly Cited
2005
Highly Cited
2005
Hemophagocytic syndrome (HPS) is characterized by an uncontrolled and poorly understood activation of T-helper 1 (Th-1… (More)
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Review
2004
Review
2004
Hemophagocytic syndrome (HPS) is a clinicopathologic entity characterized by increased proliferation and activation of benign… (More)
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Highly Cited
2000
Highly Cited
2000
Griscelli syndrome (GS, MIM 214450), a rare, autosomal recessive disorder, results in pigmentary dilution of the skin and the… (More)
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Review
2000
Review
2000
Hemophagocytic lymphohistiocytosis (HLH) is an unusual syndrome characterized by fever, splenomegaly, jaundice, and the… (More)
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Review
1998
Review
1998
Hemophagocytic lymphohistiocytosis represents a spectrum of pathogenetically different diseases in which a T-cell induced… (More)
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Review
1997
Review
1997
Hemophagocytic syndrome consists of primary and secondary HLH. Efficacy of therapeutic measures and prognosis depend on degree of… (More)
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Review
1992
Review
1992
Hemophagocytic lymphohistiocytosis, terminology that designates a syndrome that may be familial or sporadic, with or without an… (More)
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Highly Cited
1991
Highly Cited
1991
Eight cases of T-cell lymphoma localized primarily to the subcutaneous adipose tissue are described, five of which were referred… (More)
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