Denys-Drash Syndrome

Known as: Denys Drash Syndrome, Syndrome, Drash, Drash Syndrome 
A rare disorder that causes kidney failure before age 3, abnormal development of the sexual organs, and, in most cases, Wilms tumor (a type of kidney… (More)
National Institutes of Health

Papers overview

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2007
2007
Individuals with Denys-Drash syndrome (DDS) develop diffuse mesangial sclerosis, ultimately leading to renal failure. The disease… (More)
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2004
2004
While diffuse mesangial sclerosis is traditionally described as being the glomerulopathy of Denys–Drash syndrome (DDS), the… (More)
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2004
2004
We report a case of Denys-Drash syndrome, a disorder characterized by male pseudohermaphroditism, congenital nephrotic syndrome… (More)
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Review
2003
Review
2003
IMGT, the international ImMunoGeneTics database (http://imgt.cines.fr) is a high quality integrated information system… (More)
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2000
2000
The Denys-Drash syndrome is defined by the occurrence of combinations of pseudohermaphroditism, nephrotic syndrome with diffuse… (More)
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1999
1999
The Wilms tumor-suppressor gene, WT1, plays a key role in urogenital development, and WT1 dysfunction is implicated in both… (More)
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1999
1999
Denys-Drash syndrome is a rare disorder of urogenital development characterized by the association of early onset glomerulopathy… (More)
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1995
1995
We report on a newborn infant with male pseudohermaphroditism and glomerular lesions (Denys-Drash syndrome) but without Wilms… (More)
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1992
1992
Patients with the Denys-Drash syndrome (Wilms' tumor, genital anomalies, and nephropathy) have been demonstrated to carry de novo… (More)
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Highly Cited
1991
Highly Cited
1991
Denys-Drash syndrome is a rare human condition in which severe urogenital aberrations result in renal failure… (More)
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