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DNAJC19 gene

Known as: Tim14, DnaJ heat shock protein family (Hsp40) member C19, DNAJC19 
 
National Institutes of Health

Topic mentions per year

Topic mentions per year

2003-2016
02420032016

Papers overview

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2014
2014
DNAJC19, a mitochondrial cochaperone associated with cardiomyopathy, forms a complex with prohibitins to regulate cardiolipin remodeling.
Prohibitins form large protein and lipid scaffolds in the inner membrane of mitochondria that are required for mitochondrial… (More)
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2012
2012
New mutation of mitochondrial DNAJC19 causing dilated and noncompaction cardiomyopathy, anemia, ataxia, and male genital anomalies
Background:We report a new mutation in the human DNAJC19 gene that causes early onset dilated cardiomyopathy syndrome (DCMA… (More)
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2008
2008
Interaction of the J-protein heterodimer Pam18/Pam16 of the mitochondrial import motor with the translocon of the inner membrane.
Import of proteins across the inner mitochondrial membrane through the Tim23:Tim17 translocase requires the function of an… (More)
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2007
2007
Association of the Tim14.Tim16 subcomplex with the TIM23 translocase is crucial for function of the mitochondrial protein import motor.
Tim14 and Tim16 are essential components of the import motor of the mitochondrial TIM23 preprotein translocase. Tim14 contains a… (More)
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Highly Cited
2006
Highly Cited
2006
Mutation of DNAJC19, a human homologue of yeast inner mitochondrial membrane co-chaperones, causes DCMA syndrome, a novel autosomal recessive Barth syndrome-like condition.
BACKGROUND A novel autosomal recessive condition, dilated cardiomyopathy with ataxia (DCMA) syndrome, has been identified in the… (More)
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2006
2006
Structure and function of Tim14 and Tim16, the J and J-like components of the mitochondrial protein import motor.
The import motor of the mitochondrial translocase of the inner membrane (TIM23) mediates the ATP-dependent translocation of… (More)
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2006
2006
Identification of Tam41 maintaining integrity of the TIM23 protein translocator complex in mitochondria
Newly synthesized mitochondrial proteins are imported into mitochondria with the aid of protein translocator complexes in the… (More)
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2004
2004
The presequence translocase-associated protein import motor of mitochondria. Pam16 functions in an antagonistic manner to Pam18.
Transport of preproteins into the mitochondrial matrix requires the presequence translocase of the inner membrane (TIM23 complex… (More)
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Highly Cited
2003
Highly Cited
2003
Tim14, a novel key component of the import motor of the TIM23 protein translocase of mitochondria.
The TIM23 translocase mediates the deltaPsi- and ATP-dependent import of proteins into mitochondria. We identified Tim14 as a… (More)
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Highly Cited
2003
Highly Cited
2003
J protein cochaperone of the mitochondrial inner membrane required for protein import into the mitochondrial matrix.
The major Hsp70 of the mitochondrial matrix (Ssc1 in yeast) is critically important for the translocation of proteins from the… (More)
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