Primary bronchopulmonary leiomyosarcoma in childhood.
@article{Jimenez1986PrimaryBL,
title={Primary bronchopulmonary leiomyosarcoma in childhood.},
author={Jorge F. Jimenez and Edward ' Uthman and John W. Townsend and Elizabeth S. Gloster and Joanna J. Seibert},
journal={Archives of pathology \& laboratory medicine},
year={1986},
volume={110 4},
pages={
348-51
},
url={https://api.semanticscholar.org/CorpusID:24475249}
}This is believed to be the youngest patient ever reported to have PBPL, and the first such tumor, to the authors' knowledge, to be a possible cause of nonimmunologic hydrops fetalis.
19 Citations
Leiomyosarcoma of the main bronchus in a girl: A long‐time survivor with multiple lung metastases
- 2004
Medicine
Primary leiomyosarcoma of the respiratory tract is a very rare malignancy, especially in childhood, with only 15 cases in patients under 16 years old reported, but under favorable circumstances, prolonged survival is possible.
Congenital peribronchial myofibroblastic tumor: a case report and review of the literature.
- 2013
Medicine
A case of congenital peribronchial myofibroblastic tumor, in whom a right lung mass was detected in intrauterine life, with clinical, radiological and pathologic findings and a review of the literature.
Congenital peribronchial myofibroblastic tumor: case report of an asymptomatic infant with a rapidly enlarging pulmonary mass and review of the literature.
- 2015
Medicine
CPMT is a rare tumor that should be considered among other primary lung tumors of infancy (developmental, benign, and malignant) even if not detected prenatally or in the immediate postnatal period.
Unusual Presentation of Congenital Infantile Fibrosarcoma in Seven Infants with Molecular-Genetic Analysis
- 2011
Medicine
It is shown that CIFS may occur in unusual sites including visceral locations, and it is proposed that neoplasms displaying the ETV6-NTRK3 gene fusion represent the visceral components of CifS.
Congenital Peribronchial Myofibroblastic Tumor: Comparison of Fetal and Postnatal Morphology
- 2011
Medicine
This case presents a unique opportunity to examine the progression of a congenital tumor excised by prenatal and postnatal resections, and showed a marked increase in the cartilaginous component after birth as well as a decrease in cellularity and mitotic activity.
Fetal hydrops associated with congenital pulmonary myofibroblastic tumor
- 2005
Medicine
A 32‐year‐old woman referred to the authors' hospital at 29 weeks’ gestation because of severe fetal hydrops was diagnosed with a congenital pulmonary myofibroblastic tumor, the prenatal detection of which with imaging modalities has not been reported up until now.
Congenital peribronchial myofibroblastic tumor (CPMT): a case report with long term follow-up and next-generation sequencing (NGS)
- 2023
Medicine
The present patient is alive and well for 8 years after the surgery without recurrence, the longest follow-up known case of CPMT, andGene mutations in JAK2 and SMO were detected, which may be associated with the formation of C PMT.
Congenital Peribronchial Myofibroblastic Tumor: A Case Study and Literature Review
- 2013
Medicine
Although the tumor showed several malignant pathological features, recurrence was not observed in the two-year follow-up period, consistent with the benign clinical behavior of CPMT.