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long-chain-3-hydroxyacyl-CoA dehydrogenase activity

Known as: LCHAD, beta-hydroxyacyl-CoA dehydrogenase activity, long-chain 3-hydroxyacyl coenzyme A dehydrogenase activity 
Catalysis of the reaction: (S)-3-hydroxyacyl-CoA + NAD(P)+ = 3-oxoacyl-CoA + NAD(P)H + H+, where the acyl group is a long-chain fatty acid residue. A… 
National Institutes of Health

Papers overview

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2005
2005
ZusammenfassungDefizienzen der langkettigen 3-Hydroxy-Acyl-CoA-Dehydrogenase (LCHAD) sind selten. Es treten akut hypoketotische… 
2000
2000
ZusammenfassungHintergrund. Die Tandemmassenspektrometrie wurde als neue Analysetechnik für die Früherkennung angeborener…