gamma-butyrobetaine,2-oxoglutarate dioxygenase

Known as: gamma-Butyrobetaine Dioxygenase, Trimethylaminobutyrate Hydroxylase, gamma Butyrobetaine, 2 Oxoglutarate Dioxygenase 
An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE… (More)
National Institutes of Health

Papers overview

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Highly Cited
2009
Highly Cited
2009
Ethylmalonic encephalopathy is an autosomal recessive, invariably fatal disorder characterized by early-onset encephalopathy… (More)
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Highly Cited
2009
Highly Cited
2009
Mycobacterium tuberculosis, the etiological agent of TB, possesses a cholesterol catabolic pathway implicated in pathogenesis… (More)
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Highly Cited
2007
Highly Cited
2007
Genetic variants in the FTO (fat mass and obesity associated) gene have been associated with an increased risk of obesity… (More)
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Highly Cited
2004
Highly Cited
2004
Carotenoids are thought to be the precursors of terpenoid volatile compounds that contribute to flavor and aroma. One such… (More)
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Review
2002
Review
2002
Partial fatty acid oxidation inhibitors have raised great interest since they are expected to counteract a dysregulated gene… (More)
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Highly Cited
2000
Highly Cited
2000
Two genes encoding enzymes in the abscisic acid (ABA) biosynthesis pathway, zeaxanthin epoxidase (ZEP) and 9-cis-epoxycarotenoid… (More)
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Review
1998
Review
1998
In procaryotes, L-carnitine may be used as both a carbon and nitrogen source for aerobic growth, or the carbon chain may be used… (More)
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Review
1991
Review
1991
It has been suggested that early features of scurvy (fatigue and weakness) may be attributed to carnitine deficiency. Ascorbate… (More)
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Highly Cited
1990
Highly Cited
1990
Pseudomonas aeruginosa JB2 was isolated from a polychlorinated biphenyl-contaminated soil by enrichment culture containing 2… (More)
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1988
1988
A protein fraction containing gamma-butyrobetaine hydroxylase (sp.act. 1.54 mU/mg) was isolated from the rat liver by… (More)
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