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branched-chain-2-oxoacid decarboxylase activity

Known as: BCKA, branched-chain oxo acid decarboxylase activity, (3S)-3-methyl-2-oxopentanoate carboxy-lyase (2-methylbutanal-forming) 
Catalysis of the reaction: (S)-3-methyl-2-oxopentanoate + H(+) = 2-methylbutanal + CO(2). [EC:4.1.1.72, RHEA:21111]
National Institutes of Health

Papers overview

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2003
2003
Atherosclerosis, an inflammatory, proliferative disorder, is one of the leading causes of death and morbidity in the Western… 
2003
2003
Maple syrup urine disease (MSUD) is an inherited metabolic disorder biochemically characterized by the accumulation of branched… 
1999
1999
  • 1999
  • Corpus ID: 10557536
Lombardo, Yolanda B., Cynthia Serdikoff, Manikkavasagar Thamotharan, Harbhajan S. Paul, and Siamak A. Adibi. Inverse alterations… 
1987
1987
Verzweigtkettige Ketosauren konnten Fortschritte bei der Behandlung stickstoffakkumulierender Erkrankungen oder von Zustanden mit… 
1986
1986
The splanchnic balances of branched-chain amino acids (BCAA) and ketoacids (BCKA) concentrations were compared in rats fed a 15… 
1985
1985
Branched chain amino acid (BCAA) transaminase activity increased in both the mitochondrial and supernatant fractions of brain… 
1983
1983
The changes in serum branched-chain alpha-keto acid (BCKA) and plasma amino acid concentrations, in response to a therapeutic… 
1983
1983
Branched-chain alpha-keto acid (BCKA) supplements are used as a nitrogen-free source of branched-chain amino acids (BCAA) in… 
1982
1982
To detect heterozygotes for maple-syrup-urine disease (MSUD), activities of branched-chain-alpha-ketoacid (BCKA) dehydrogenase… 
1981
1981
The effect of an oral glucose tolerance test (oGTT) on serum levels of branched-chain keto acids (BCKA), i.e. alpha-keto…