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Progressive intrahepatic cholestasis (disorder)

Known as: PFIC1, cholestasis familial intrahepatic, Byler's syndrome 
A genetic syndrome affecting infants and children. It is characterized by chronic intrahepatic cholestasis usually progressing to cirrhosis within… 
National Institutes of Health

Related topics

Related topics

15 relations
ATP8B1, 2097T-C, +2Autosomal recessive inheritanceCholestasis, Progressive Familial Intrahepatic, 2Congenital hypofibrinogenemia

Broader (2)

CholestasisIntrahepatic Cholestasis

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
2009
2009
Interventional percutaneous trans‐splenic approach in the management of portal venous occlusion after living donor liver transplantation
A 2-year-old Chinese boy with progressive familial intrahepatic cholestasis type II–related end-stage liver disease underwent… 
2000
2000
[An autopsy case of intrahepatic cholangiocarcinoma producing granulocyte-colony stimulating factor].
1997
1997
Byler’s syndrome
Editor,—The report of Byler’s syndrome with raised sweat electrolytes in an Irish traveller kindred1interests us, as we have… 
1997
1997
Lipiodol-CT for hepatocellular carcinoma
Lencioni et al. have nicely presented a positive predictive value of Lipiodol CT for intrahepatic metastasis of hepatocellular… 
1994
1994
Intrahepatic subcapsular biloma
Bile leaks leading to bilomas in the subhepatic space are amongst the most common complications of laparoscopic cholecystectomy… 
1992
1992
Comparison between diploid and aneuploid hepatocellular carcinomas: A flow cytometric study
Nuclear DNA content of hepatocellular carcinoma (HCC) was estimated by flow cytometry after hepatic resection in 91 patients… 
1976
1976
Cholestasis associated with administration of L-amino acids and dextrose solutions.
Infants of very low birth weight who require prolonged assisted ventilation are unable to tolerate oral feedings. To provide and… 
1973
1973
Intrahepatic cholangiojejunostomy in the management of malignant biliary obstruction.
1968
1968
A case of familial intrahepatic cholestasis.
A case of intrahepatic cholestasis with mental and growth retardation, which was considered to be familial, was presented. The… 
1949
1949
Partial Hepatectomy with Intrahepatic Cholangiojejunostomy : A Useful Addition to Technical Methods for the Management of Common Duct Stricture.