Phacomatosis pigmentokeratotica

Germline mutations in the oncogene HRAS cause syndromes with systemic and cutaneous features, notably Costello syndrome (CS).1… Expand

Phacomatosis pigmentokeratotica (PPK) is a rare epidermal nevus syndrome characterized by the co-occurrence of a nevus sebaceous… Expand

Cutaneous symptoms in some patients with clinical picture of Schimmelpenning-Feuerstein-Mims syndrome can include a speckled… Expand

TO THE EDITOR We have examined a patient with a subtype of phacomatosis pigmentokeratotica (PPK) who had agminated melanocytic… Expand

Phacomatosis pigmentokeratotica (PPK) is characterized by the co-existence of epidermal nevi and large segmental speckled… Expand

Phacomatosis pigmentokeratotica (PPK) is a rare syndrome defined by the association of an organoid nevus occasionally with… Expand

© 2011 The Authors. doi: 10.2340/00015555-1133 Journal Compilation © 2011 Acta Dermato-Venereologica. ISSN 0001-5555 Epidermal… Expand

Phacomatosis pigmentokeratotica (PP) is a mosaic disorder that represents a distinct epidermal naevus syndrome. Its defining… Expand

Phacomatosis pigmentokeratotica (PPK) represents a specific "twin nevus" syndrome in which a speckled lentiginous nevus (SLN) is… Expand

We present a patient with phacomatosis pigmentokeratotica (PPK) who developed several basal cell carcinomas on epidermal nevus… Expand