Phacomatosis pigmentokeratotica

In phacomatosis pigmentokeratotica, papular nevus spilus coexists with nevus sebaceus. The disorder was thought to be a didymosis… (More)

Phacomatosis pigmentokeratotica (PPK) is a rare epidermal nevus syndrome characterized by the co-occurrence of a sebaceous nevus… (More)

Phacomatosis pigmentokeratotica is characterized by the coexistence of an organoid epidermal naevus, follow-ing Blaschko's lines… (More)

This is a follow-up report on a boy with phacomatosis pigmentokeratotica. At the age of 10 years he had, in addition to a… (More)

Phacomatosis pigmentokeratotica (PP) is a mosaic disorder that represents a distinct epidermal naevus syndrome. Its defining… (More)

Phacomatosis pigmentokeratotica is a rare syndrome defined by the association of an organoid nevus occasionally with sebaceous… (More)

Phacomatosis pigmentokeratotica is a rare but highly characteristic disease defined by the occurrence of an organoid naevus with… (More)

The name epidermal nevus syndrome could be applied to a group of clinically and histopathologically different entities as has… (More)

We report a case of a congenital nevus sebaceus with numerous brown macules and papules in the left auricular region. In the same… (More)

We describe a 10-year-old girl affected with a speckled lentiginous nevus and an epidermal nevus of the organoid type on… (More)