Skip to search formSkip to main contentSkip to account menu

N-sulfoglucosamine sulfohydrolase activity

Known as: N-sulfo-D-glucosamine sulfohydrolase activity, N-sulphoglucosamine sulphohydrolase activity, heparin sulfamidase activity 
Catalysis of the reaction: N-sulfo-D-glucosamine + H2O = D-glucosamine + sulfate. [EC:3.10.1.1]
National Institutes of Health

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
2019
2019
Mucopolysaccharidosis (MPS) IIIA, also known as Sanfilippo syndrome type A, is a severe, progressive disease that affects the… 
Highly Cited
2013
Highly Cited
2013
Mucopolysaccharidoses type IIIA (MPS‐IIIA) is a neurodegenerative lysosomal storage disorder (LSD) caused by inherited defects of… 
Highly Cited
2004
Highly Cited
2004
Mucopolysaccharidosis type IIIA (SanÐlippo A; McKusick 25290) is caused by a deÐciency of lysosomal sulphamidase activity (EC 3… 
2003
2003
Sanfilippo A syndrome, mucopolysaccharidosis type IIIA, is caused by a deficiency of heparan sulphamidase activity, and usually… 
Highly Cited
1996
Highly Cited
1996
Summary4-Methylumbelliferyl-α-d-N-sulphoglucosaminide (MU-α-GlcNS) was synthesized and shown to be a substrate for the lysosomal… 
1993
1993
Early amniocentesis performed at 13 weeks gestation was utilized to obtain amniocytes for culture. Sonicates of cultured… 
1986
1986
Human sulphamate sulphohydrolase was purified at least 20,000-fold to homogeneity from liver with a three-step four-column… 
1981
1981
1. Sulphamidase activity was assayed by incubation of the radiolabelled disaccharide O-(alpha-2-sulphamino-2-deoxy-D… 
Highly Cited
1974
Highly Cited
1974
A sulphamidase activity present in rat spleen capable of hydrolysing N-[(35)S]sulphated heparin was studied. This activity was… 
1971
1971