Lymphohistiocytosis

 
National Institutes of Health

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
2015
2015
The hyperinflammatory syndrome hemophagocytic lymphohistiocytosis can occur in the context of malignancies. Malignancy-triggered… (More)
Is this relevant?
2013
2013
X-linked inhibitor of apoptosis (XIAP) deficiency caused by mutations in BIRC4 was initially described in patients with X-linked… (More)
  • table 1
  • figure 1
Is this relevant?
Highly Cited
2010
Highly Cited
2010
Recent experience suggests that reduced-intensity conditioning (RIC) regimens can improve the outcomes of patients with… (More)
  • table 1
  • table 2
  • figure 1
  • table 3
  • table 4
Is this relevant?
Review
2008
Review
2008
Hemophagocytic lymphohistiocytosis is a rare condition characterized by highly stimulated but inactive immune response. The… (More)
  • table 1
  • figure 1
  • table 2
  • figure 2
Is this relevant?
2008
2008
The clinical syndromes of hemophagocytic lymphohistiocytosis (HLH) and macrophage activation syndrome (MAS) are both… (More)
Is this relevant?
2007
2007
Perforin gene (PRF1) mutations cause the primary form of hemophagocytic lymphohistiocytosis (HLH). We report a genetic defect of… (More)
  • figure 1
  • figure 2
Is this relevant?
Review
2005
Review
2005
Haemophagocytic syndrome (HS), also referred to as haemophagocytic lymphohistiocytosis or macrophage activation syndrome… (More)
  • table 1
  • table 2
  • figure 1
  • figure 2
  • figure 3
Is this relevant?
Review
2003
Review
2003
Perforin gene (PRF1) mutations appear to occur in about 30% of patients with haemophagocytic lymphohistiocytosis (HLH). We tested… (More)
Is this relevant?
Highly Cited
2001
Highly Cited
2001
The hemophagocytic lymphohistiocytoses (HLH) comprise a heterogeneous group of disorders characterized by dysregulated activation… (More)
  • figure 2
  • figure 1
Is this relevant?
Review
1992
Review
1992
Hemophagocytic lymphohistiocytosis, terminology that designates a syndrome that may be familial or sporadic, with or without an… (More)
Is this relevant?