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Long chain acyl-CoA dehydrogenase deficiency

Known as: Long-chain acyl-CoA dehydrogenase deficiency, Acyl-Coa Dehydrogenase, Long-Chain, Deficiency of, Acyl-CoA Dehydrogenase, Long-Chain Deficiency 
A genetic disorder characterized by deficiency of the enzyme long-chain acyl-coenzyme A dehydrogenase that metabolizes long-chain fatty acids. Signs… 
National Institutes of Health

Related topics

Related topics

4 relations
Enzyme DeficiencyInborn Errors of Metabolism

Broader (2)

Lipid Metabolism, Inborn ErrorsLong-Chain-Acyl-CoA Dehydrogenase

Papers overview

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2017
2017
A Dual Agonist of Farnesoid X Receptor (FXR) and the G protein-coupled Receptor TGR5, INT-767, Slows Down Age-Related Kidney Disease in Mice
Even in healthy individuals, renal function gradually declines during aging. However, an observed variation in the rate of this… 
2015
2015
Tin ( IV ) Anl imonatc as a Lcad-Selective Cation Exchanger : Synthesis , Characterization , and Analytical Applications
A new phase of a Iraci-selef live calion exdiange material, tin(I\'.) antimonate has been prepared, which possesses a gtHxl… 
2011
2011
Myocardial pyruvate dehydrogenase flux in long-chain acyl-CoA dehydrogenase knock-out mice
Introduction: Patients affected by long-chain fatty acid β-oxidation (FAO) disorders may present with hypertrophic cardiomyopathy… 
Review
2001
Review
2001
Lipid metabolism in the heart —Contribution of BMIPP to the diseased heart—
Lipid contributes greatly in cardiac metabolism to produce high energy ATPs, and is suggested to be related to the progression… 
2000
2000
Detection and Assessment Using Positron Emission Tomography of Genetically OSTI
The aim of this project was to determine whether abnormalities in myocardial fatty acid metabolism could be delineated using…