Isovalerylglycine
National Institutes of Health
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Summary: The abnormal metabolites-adipic, suberic, and sebacic acids-were detected in large amounts in the urine of a boy during…
Summary: When amino acids were infused at a rate of 4 g/kg/day, an infant with hypoglycemia, metabolic acidemia and chronic…
Repeated episodes of hypoglycemia accompanied by elevated serum concentrations of free fatty acid without ketosis, fatty…
Extract: A 7-year-old girl with periodic acidosis, lethargy, and coma beginning during the 1st year of life was studied. Episodes…