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Hepatic Fibrosis, Congenital

Known as: Congenital Hepatic Fibrosis, Congenital Fibrose Liver, congenital fibrosis liver 
A congenital disorder usually inherited in an autosomal recessive pattern. It affects the hepatobiliary system and the kidneys. It is characterized… 
National Institutes of Health

Related topics

Related topics

10 relations
COACH syndromeCongenital AbnormalityGastrointestinal systemHepatobiliary System

Broader (4)

FibrosisFibrosis, LiverGenetic Diseases, InbornLiver Cirrhosis

Papers overview

Semantic Scholar uses AI to extract papers important to this topic.
Review
1998
Review
1998
Caroli's disease: report of 10 cases in children and adolescents in southern Brazil.
1995
1995
Long‐term studies on congenital hepatic fibrosis in children
Congenital hepatic fibrosis (CHF) is an inherited malformation, defined pathologically by bands of fibrous tissue within the… 
1992
1992
Spastic paraparesis associated with portal‐systemic venous shunting due to congenital hepatic fibrosis
We report a case of progressive spastic paraparesis in a 45-year-old man with total portal-systemic shunting, which developed… 
1991
1991
Congenital hepatic fibrosis in Saudi Arabia.
Congenital hepatic fibrosis (CHF) is a recognized cause of portal hypertension with oesophageal varices, gastro-intestinal… 
1990
1990
Polycystic kidney of autosomal dominant inheritance, polycystic liver and congenital hepatic fibrosis in a single kindred.
A family with clear evidence of concomitant congenital hepatic fibrosis, polycystic liver and adult-type polycystic kidney is… 
1986
1986
An autosomal recessive mental retardation syndrome with hepatic fibrosis and renal cysts.
Two sisters had developmental retardation and congenital hepatic fibrosis. One, 23 years old, had facial anomalies reminiscent of… 
1978
1978
Kidney polycystic disease in adult congenital hepatic fibrosis.
Excerpt Congenital hepatic fibrosis and the adult type of polycystic disease of liver and kidneys are regarded as different… 
1977
1977
Congenital hepatic fibrosis: asymptomatic adults without renal anomaly.
Two cases with the pathologic changes of congenital hepatic fibrosis are described in asymptomatic adults without renal anomaly… 
Review
1973
Review
1973
Congenital hepatic fibrosis--is it a single clinical entity?
1964
1964
CONGENITAL FIBROSIS OF THE VASTUS INTERMEDIUS MUSCLE.
1. The cases of six Chinese children affected by so-called congenital fibrosis of the vastus intermedius muscle are described… 
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