Congenital sensorineural hearing loss

Known as: Congenital perceptive deafness, Congenital neurosensory deafness, Hearing loss, congenital sensorineural 
A type of hearing impairment caused by an abnormal functionality of the cochlear nerve with congenital onset. [HPO:probinson]
National Institutes of Health

Papers overview

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2012
2012
Hearing loss is the most common sensory disability with an incidence of one over 1000 newborns. Hearing loss may be caused by… (More)
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2010
2010
Received August 18, 2008 accepted after revision March 14, 2009. 1Both authors: Department of Radiology, Children’s National… (More)
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2007
2007
The route of the cochlear nerve can be imaged using computed tomography (CT) or magnetic resonance imaging (MRI). To gain… (More)
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2002
2002
OBJECTIVE To examine the yield of ophthalmologic examination in the diagnostic workup of unexplained sensorineural hearing loss… (More)
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Highly Cited
1998
Highly Cited
1998
OBJECTIVE The advent of technologic improvements in assessing the hearing of newborn infants has made possible the implementation… (More)
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Highly Cited
1995
Highly Cited
1995
USHER syndrome represents the association of a hearing impairment with retinitis pigmentosa1 and is the most frequent cause of… (More)
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Highly Cited
1992
Highly Cited
1992
Congenital cytomegalovirus (CMV) infection is a major public health problem because 30,000 to 40,000 neonates with the infection… (More)
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Review
1992
Review
1992
The inner ear is composed of the membranous labyrinth and the osseous labyrinth (1). The membranous labyrinth has two major… (More)
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1987
1987
Prospective studies have suggested that about 108 children with congenital cytomegalovirus (CMV) infection and bilateral… (More)
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1984
1984
The ears of 47 selected patients with congenital sensorineural hearing loss were examined with complex-motion tomography. The… (More)
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