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4a-hydroxytetrahydrobiopterin dehydratase
Known as:
pterin-4a-carbinolamine dehydratase
, pterin-4alpha-carbinolamine dehydratase
, dimerization cofactor of HNF-1alpha
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National Institutes of Health
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Related topics
Related topics
4 relations
4a-hydroxytetrahydrobiopterin dehydratase activity
Broader (1)
Hydro-Lyases
Narrower (2)
PCBD1 protein, human
Pcbd1 protein, mouse
Papers overview
Semantic Scholar uses AI to extract papers important to this topic.
Highly Cited
2014
Highly Cited
2014
A protein with an inactive pterin-4a-carbinolamine dehydratase domain is required for Rubisco biogenesis in plants.
Leila Feiz
,
R. Williams-Carrier
,
Susan Belcher
,
M.A.E. Montano
,
A. Barkan
,
D. Stern
The Plant journal : for cell and molecular…
2014
Corpus ID: 37979314
Ribulose-1,5-bisphosphate carboxylase/oxygenase (Rubisco) plays a critical role in sustaining life by catalysis of carbon…
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Review
2011
Review
2011
Tetrahydrobiopterin: biochemistry and pathophysiology.
E. Werner
,
N. Blau
,
B. Thöny
The Biochemical journal
2011
Corpus ID: 4849923
BH4 (6R-L-erythro-5,6,7,8-tetrahydrobiopterin) is an essential cofactor of a set of enzymes that are of central metabolic…
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Highly Cited
2009
Highly Cited
2009
Exhaustive analysis of BH4 and dopamine biosynthesis genes in patients with Dopa-responsive dystonia.
F. Clot
,
D. Grabli
,
+23 authors
A. Brice
Brain : a journal of neurology
2009
Corpus ID: 18009099
Dopa-responsive dystonia is a childhood-onset dystonic disorder, characterized by a dramatic response to low dose of L-Dopa. Dopa…
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Highly Cited
2005
Highly Cited
2005
International database of tetrahydrobiopterin deficiencies
N. Blau
,
I. Barnes
,
J. Dhondt
Journal of Inherited Metabolic Disease
2005
Corpus ID: 21512231
SummaryApproximately 2% of newborns with hyperphenylalaninaemia are deficient in tetrahydrobiopterin. Selective screening must be…
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Highly Cited
2004
Highly Cited
2004
Activation/deactivation of acetylcholinesterase by H2O2: more evidence for oxidative stress in vitiligo.
K. Schallreuter
,
S. Elwary
,
N. J. Gibbons
,
H. Rokos
,
J. Wood
Biochemical and biophysical research…
2004
Corpus ID: 1717215
Highly Cited
2002
Highly Cited
2002
HNF-1α G319S, a transactivation-deficient mutant, is associated with altered dynamics of diabetes onset in an Oji-Cree community
B. Triggs-Raine
,
R. Kirkpatrick
,
+8 authors
R. Hegele
Proceedings of the National Academy of Sciences…
2002
Corpus ID: 29906267
The prevalence of type 2 diabetes mellitus in the Oji-Cree of northwestern Ontario is the third highest in the world. A private…
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Review
2002
Review
2002
Disorders of tetrahydrobiopterin metabolism and their treatment.
H. Shintaku
Current drug metabolism
2002
Corpus ID: 11743250
Tetrahydrobiopterin (BH4) deficiencies are disorders affecting phenylalanine metabolism in liver and neurotransmitters…
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Review
2000
Review
2000
Tetrahydrobiopterin biosynthesis, regeneration and functions.
B. Thöny
,
G. Auerbach
,
N. Blau
The Biochemical journal
2000
Corpus ID: 218978
Tetrahydrobiopterin (BH(4)) cofactor is essential for various processes, and is present in probably every cell or tissue of…
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Highly Cited
1999
Highly Cited
1999
Metabolic activation of dacarbazine by human cytochromes P450: the role of CYP1A1, CYP1A2, and CYP2E1.
J. Reid
,
M. Kuffel
,
J. Miller
,
R. Rios
,
M. Ames
Clinical cancer research : an official journal of…
1999
Corpus ID: 182929
Dacarbazine (DTIC), a widely used anticancer agent, is inactive until metabolized in the liver by cytochromes P450 to form the…
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Highly Cited
1989
Highly Cited
1989
Evidence for the formation of the 4a-carbinolamine during the tyrosine-dependent oxidation of tetrahydrobiopterin by rat liver phenylalanine hydroxylase.
M. Davis
,
S. Kaufman
The Journal of biological chemistry
1989
Corpus ID: 31142089
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