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4a-hydroxytetrahydrobiopterin dehydratase

Known as: pterin-4a-carbinolamine dehydratase, pterin-4alpha-carbinolamine dehydratase, dimerization cofactor of HNF-1alpha 
National Institutes of Health

Related topics

Related topics

4 relations
4a-hydroxytetrahydrobiopterin dehydratase activity

Broader (1)

Hydro-Lyases

Narrower (2)

PCBD1 protein, humanPcbd1 protein, mouse

Papers overview

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2016
2016
Four Years of Diagnostic Challenges with Tetrahydrobiopterin Deficiencies in Iranian Patients.
Hyperphenylalaninemia (HPA) is a condition caused by tetrahydrobiopterin (BH4) and phenylalanine hydroxylase (PAH) deficiencies… 
2006
2006
GHP, a new c‐type green heme protein from Halochromatium salexigens and other proteobacteria
We have isolated a minor soluble green‐colored heme protein (GHP) from the purple sulfur bacterium, Halochromatium salexigens… 
2000
2000
Pterin-4alpha-carbinolamine dehydratase in rat brain. I. Patterns of co-localization with tyrosine hydroxylase.
2000
2000
Hyperphenylalaninemia and 7-pterin excretion associated with mutations in 4a-hydroxy-tetrahydrobiopterin dehydratase/DCoH: analysis of enzyme activity in intestinal biopsies.
Hyperphenylalaninemia, which can cause neurological disorders and mental retardation, results from a mutation in phenylalanine… 
1999
1999
Characterization of expression of the gene for human pterin carbinolamine dehydratase/dimerization cofactor of HNF1.
Pterin carbinolamine dehydratase/dimerization cofactor of HNF1 (PCD/DCoH) is a dual-function protein. In the cytoplasm it acts as… 
Review
1996
Review
1996
Tetrahydrobiopterin and inherited hyperphenylalaninemias.
Tetrahydrobiopterin deficiency, a variant of hyperphenylalaninemia, may be caused by deficiency of one of the following enzymes… 
1995
1995
Three‐dimensional structure of the bifunctional protein PCD/DCoH, a cytoplasmic enzyme interacting with transcription factor HNF1.
The bifunctional protein pterin‐4a‐carbinolamine dehydratase (PCD)/dimerization cofactor of HNF1 (DCoH) is a cytoplasmic enzyme… 
1995
1995
Human pterin-4 alpha-carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor-1 alpha. Characterization and kinetic analysis of wild-type and mutant enzymes.
Pterin-4a-carbinolamine dehydratase/dimerization cofactor for hepatocyte nuclear factor-1 alpha is a protein with two different… 
1993
1993
Synthesis, chemical reactivity, and antitumor evaluation of congeners of carmethizole hydrochloride, an experimental "acylated vinylogous carbinolamine" tumor inhibitor.
A series of analogues of 4,5-bis(((N-methylcarbamoyl)oxy)methyl)-1-methyl-2-(methylthio)-im idazole (1, carmethizole) were… 
1993
1993
Spectroscopic characterization of human liver pterin 4a-carbinolamine dehydratase.
The hepatic hydroxylation of phenylalanine catalyzed by phenylalanine hydroxylase (PAH), is dependent on tetrahydrobiopterin (BH4… 
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