3-methyl-2-oxobutanoate dehydrogenase (lipoamide) complex

Known as: BCADH, branched-chain alpha-ketoacid dehydrogenase complex, 3-methyl-2-oxobutanoate dehydrogenase (lipoamide) complex location 
A protein complex that catalyzes the reaction 3-methyl-2-oxobutanoate + lipoamide = S-(2-methylpropanoyl)-dihydrolipoamide + carbon dioxide (CO2… (More)
National Institutes of Health

Topic mentions per year

Topic mentions per year

1982-2013
024619822013

Papers overview

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2011
2011
The purified mammalian branched-chain α-ketoacid dehydrogenase complex (BCKDC), which catalyzes the oxidative decarboxylation of… (More)
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2006
2006
The dihydrolipoamide acyltransferase (E2b) component of the branched-chain alpha-ketoacid dehydrogenase complex forms a cubic… (More)
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2004
2004
The human mitochondrial branched-chain alpha-ketoacid dehydrogenase complex (BCKDC) is a 4 MDa macromolecular machine comprising… (More)
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1997
1997
Five mitochondrial protein kinases, all members of a new family of protein kinases, have now been identified, cloned, expressed… (More)
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1995
1995
The branched-chain alpha-ketoacid dehydrogenase complex, catalyst for the rate-limiting step of branched-chain amino acid… (More)
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1992
1992
A cDNA for branched-chain alpha-ketoacid dehydrogenase kinase was cloned from a rat heart cDNA library. The cDNA had an open… (More)
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1991
1991
Maple syrup urine disease (MSUD) results from an inborn metabolic error caused by a deficiency of the branched-chain alpha… (More)
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1990
1990
The hepatic branched-chain alpha-ketoacid dehydrogenase complex plays an important role in regulating branched-chain amino acid… (More)
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1990
1990
Branched-chain alpha-ketoacid dehydrogenase kinase was purified to homogeneity from rat liver and rat heart. The initial step was… (More)
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1986
1986
The branched-chain alpha-ketoacid dehydrogenase complex, like the pyruvate dehydrogenase complex, is an intramitochondrial enzyme… (More)
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