Vanishing Lung Syndrome (Giant Bullous Emphysema): CT Findings in 7 Patients and a Literature Review

@article{Sharma2009VanishingLS,
  title={Vanishing Lung Syndrome (Giant Bullous Emphysema): CT Findings in 7 Patients and a Literature Review},
  author={Nidhi Sharma and Al Mamoon Justaniah and Jeffrey P Kanne and Jud W. Gurney and Tan Lucien H Mohammed},
  journal={Journal of Thoracic Imaging},
  year={2009},
  volume={24},
  pages={227-230}
}
PURPOSE we reviewed the imaging findings in 7 patients with idiopathic giant bullous emphysema. [] Key Method On HRCT scans, the size, location, and distribution of the bullae were documented and categorized as either subpleural or central. RESULTS The HRCT scan findings in all 7 study patients included numerous bullae ranging in size from a few centimeters in diameter to giant bullae nearly filling an entire hemithorax, mimicking a pneumothorax.

Symptomatic unilateral idiopathic giant bullous emphysema : a case report

TLDR
V VATS bullectomy was shown to be an effective therapeutic option, allowing re-expansion of compressed lung tissue and complete resolution of symptoms, in a solitary giant bulla occurring without major risk factors or underlying lung disease.

Vanishing Lung Syndrome: A Rare Entity -

TLDR
A 20-year-old male was admitted with complaints of shortness of breath, chest pain, sweating, and tachycardia and chest X-ray and chest CT images revealed the presence of giant bullae occupying the left hemithorax and pneumothorax.

A rare case of vanishing lung syndrome with pneumothorax: importance of computed tomography

TLDR
This case exemplifies role of HRCT thorax in timely diagnosis and planning appropriate treatment of VLS, and is reported in a 40-year-old male patient, who was a chronic smoker for past 20 years.

Vanishing lung syndrome vs emphysematous bulla: Two interesting cases

TLDR
A rare case of a 28-year-old female patient who had no history of smoking, presented with chronic cough, expectoration and weight loss, is described, which revealed findings suggestive of giant bullous disease/vanishing lung syndrome.

Vanishing lung syndrome in one family: five cases with a 20-year follow-up.

TLDR
The present study suggests that vanishing lung syndrome may be associated with autosomal dominant and recessive genetic inheritance.

The vanishing lung: an important cause of hyperlucency on chest radiograph.

TLDR
This work describes two cases with this condition that presented acutely and discusses the management of bullous emphysema, a rare condition characterised by large asymmetric bullae with upper lobe predominance.

Tuberculosis-related giant bullae mimicking tension pneumothorax

TLDR
A 54-year-old man presented to the emergency department with a 2-day history of worsening dyspnea on exertion and was diagnosed with TB-related giant pulmonary bullae, and bullectomy was scheduled.

PRIMARY BULLOUS LUNG DISEASE - A CASE REPORT -

TLDR
A case of bullous lung disease is presented in a sixty five year old man with a clinical presentation of pneumothorax and the diagnosis was established by high resolution computed tomography of the chest.

Vanishing Lung Syndrome and Lung Volume Reduction Surgery-A Case Report

TLDR
This case demonstrated that giant bullae can be successfully managed with surgical resection, and that their size can be determined by different techniques, including chest CT and lung volume measurements.

Giant bulla or pneumothorax

TLDR
It is very important to make an early and quick diagnosis between giant bulla and pneumothorax before contemplating intervention, and right lung volume reduction preferably through a small incision should be the preferred treatment in this patient.
...

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TLDR
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TLDR
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