Valvular heart disease in four patients with Maroteaux-Lamy syndrome.

Abstract

BACKGROUND Maroteaux-Lamy syndrome is a lysosomal storage disease of mucopolysaccharide metabolism (MPS type VI) that may involve the mitral and aortic valves. Affected patients have other skeletal and oropharyngeal malformations that complicate anesthetic and surgical management. METHODS AND RESULTS The present report describes the clinical… (More)

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@article{Tan1992ValvularHD, title={Valvular heart disease in four patients with Maroteaux-Lamy syndrome.}, author={C. T. Tan and Hartzell Vernon Schaff and Fletcher A. Miller and William D. Edwards and Pamela S Karnes}, journal={Circulation}, year={1992}, volume={85 1}, pages={188-95} }