Utilisation of amino acid mixtures in adolescents with phenylketonuria

  title={Utilisation of amino acid mixtures in adolescents with phenylketonuria},
  author={Eberhard M{\"o}nch and M. E. Herrmann and Herbert Br{\"o}sicke and A. Sch{\"o}ffer and Martina Keller},
  journal={European Journal of Pediatrics},
The nutritional regimen of patients with phenylketonuria (PKU) comprises a diet of natural proteins and phenylalanine(Phe)-free amino acid (AA) mixture. The main daily protein requirement is covered by a Phe-free A A mixture. In an adult with PKU, the consumption of the daily AA requirement in one single dose at breakfast caused nausea and vomiting. Therefore, four studies were designed to investigate the adverse and metabolic effects resulting from large intakes of AA mixtures used in the… CONTINUE READING
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Dependence of the utilisation of a phenylalanine-free amino acid mixture on different amounts of single dose ingested. A case report

  • M-E Herrmann, HG Br6sicke, M Keller, E M6nch, H Helge
  • Eur J Pediatr
  • 1994
1 Excerpt

Influence of single dose amount of amino acid mixtures on the nitrogen retention in patients with phenylketonuria

  • A Schoeffer, M-E Herrmann, HG Br6sicke, E M6nch
  • J Nutr Med
  • 1994
1 Excerpt

Phenylalaninfreie Aminos/~urenmi- schung: Stoffwechselwirkung in Abh~in- gigkeit von der Einzeldosis

  • M-E Herrmann, E M6nch, M Reinbacher, W Kohlen
  • HG
  • 1991
2 Excerpts

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