Urbach-Wiethe Disease(Lipoid Proteinosis)

  title={Urbach-Wiethe Disease(Lipoid Proteinosis)},
  author={C. C. Staut and T. Naidich},
  journal={Pediatric Neurosurgery},
  pages={212 - 214}
  • C. C. Staut, T. Naidich
  • Published 1998
  • Medicine
  • Pediatric Neurosurgery
  • reasoning, cognitive flexibility, judgment, decision making and planning all appear to be reduced in these patients [17]. Psychomotor seizures with olfactory hallucinations, déjà vu, automatisms such as lip smacking and facial grimacing, rage attacks and paranoia have all been reported [13, 18] in patients with temporal lobe calcifications but are not seen in all patients with such calcifications [13]. Seizures rarely begin before adulthood [3]. In Heyl’s [12] series of 20 patients, 4 had… CONTINUE READING

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