Update on Wilson disease.

@article{Aggarwal2013UpdateOW,
  title={Update on Wilson disease.},
  author={Annu Aggarwal and Mohit H Bhatt},
  journal={International review of neurobiology},
  year={2013},
  volume={110},
  pages={313-48}
}
Wilson disease (WD) is an inherited disorder of chronic copper toxicosis characterized by excessive copper deposition in the body, primarily in the liver and the brain. It is a progressive disease and fatal if untreated. Excessive copper accumulation results from the inability of liver to excrete copper in bile. Copper is an essential trace metal and has a crucial role in many metabolic processes. Almost all of the body copper is protein bound. In WD, the slow but relentless copper accumulation… CONTINUE READING

References

Publications referenced by this paper.
Showing 1-10 of 93 references

lates of osseomuscular disability in Wilson’s disease.Movement Disorders

A. Aggarwal, A. Nagral, G. Jankharia, N. Aggarwal, M. Bhatt
Movement Disorders, • 2009
View 6 Excerpts
Highly Influenced

Wilson's disease.

Archives of neurology • 1988
View 8 Excerpts
Highly Influenced

Wilson’s disease. Major problems in internal medicine

I. H. Scheinberg, I. Sternlieb
1984
View 19 Excerpts
Highly Influenced

Role of genotyping in Wilson's disease.

Journal of hepatology • 2009
View 3 Excerpts
Highly Influenced

The conquest of Wilson's disease.

Brain : a journal of neurology • 2009
View 5 Excerpts
Highly Influenced

Treatment of Wilson's disease with zinc XVI: treatment during the pediatric years.

The Journal of laboratory and clinical medicine • 2001
View 1 Excerpt
Highly Influenced

Dystonic opisthotonus: A “red flag” for neurodegeneration with brain iron accumulation syndromes?

Movement disorders : official journal of the Movement Disorder Society • 2013
View 1 Excerpt

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