Two generations with familial thrombotic thrombocytopenic purpura.

  • Rui G Rodrigues
  • Published 2006 in International journal of clinical practice
Thrombotic thrombocytopenic purpura (TTP) is a rare multi-system disease characterised by the pentad of microangiopathic haemolytic anaemia, thrombocytopenia, renal dysfunction, fever and neurologic changes. A hereditary form of recurrent familial TTP has been described, which usually presents in adolescence or early adulthood and can lead to recurrent or… CONTINUE READING