Treatment of inherited platelet disorders.

  title={Treatment of inherited platelet disorders.},
  author={Uri Seligsohn},
  journal={Haemophilia : the official journal of the World Federation of Hemophilia},
  volume={18 Suppl 4},
For patients affected by severe inherited platelet dysfunctions, e.g. Glanzmann thrombasthenia (GT) or Bernard-Soulier syndrome (BSS), platelet transfusion is frequently needed for controlling spontaneous bleeding, and is always needed when trauma occurs or surgery is performed. For the mild-to-moderate bleeding entities, e.g. storage pool disease, thrombaxane A2 receptor defect, platelet transfusion is usually unnecessary. Transfusion of platelets should be used selectively and sparingly… CONTINUE READING


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